Research & Literature

Life-threatening onset of systemic vasculitis requiring intensive care unit admission: a case series.

Monti S, Montecucco C, Pieropan S, et al.

Clinical and experimental rheumatology 2015; (33(2 Suppl 89)):S-126-31 doi:10.1136/annrheumdis-2015-eular.5151.

GRANULOMATOSIS WITH POLYANGIITIS IN PUERTO RICO: CASE REPORTS.

Aranguren L, Izquierdo NJ, Oliver A

Boletin de la Asociacion Medica de Puerto Rico 2014; (106(4)):31-4.

Atypical Endobronchial Carcinoid with Postobstructive Pneumonia Obscuring the Diagnosis of Granulomatosis with Polyangiitis.

Ali R, Baldeo C, Onyenekwe J, et al.

Case reports in rheumatology 2015; (2015()):513602 doi:10.1155/2015/513602.

Wegener granulomatosis as possible cause of vertigo: case report and review.

Goderis J, De Schepper S, Vannieuwenhuyze P, Schmelzer B

B-ENT 2015; (11(1)):67-72.

Clinic manifestations in granulomatosis with polyangiitis.

Greco A, Marinelli C, Fusconi M, et al.

International journal of immunopathology and pharmacology 2016; (29(2)):151-9 doi:10.1177/0394632015617063.

Granulomatosis with polyangiitis and facial palsy: Literature review and insight in the autoimmune pathogenesis.

Iannella G, Greco A, Granata G, et al.

Autoimmunity reviews 2016; (15(7)):621-31.

RITUXIMAB: THE DRUG THAT NEVER FAILS TO SURPRISE!

Seth AA, Patel S, Gangam MA, Hayat SQ

The Journal of the Louisiana State Medical Society : official organ of the Louisiana State Medical Society 2015; (167(3)):153.

Myeloperoxidase-Antineutrophil Cytoplasmic Antibody (ANCA)-Positive and ANCA-Negative Patients With Granulomatosis With Polyangiitis (Wegener's): Distinct Patient Subsets.

Miloslavsky EM, Lu N, Unizony S, et al.

Arthritis & rheumatology (Hoboken, N.J.) 2016; (68(12)):2945-2952 doi:10.1002/art.39812.

Overview of the Pathogenesis of ANCA-Associated Vasculitis.

Xiao H, Hu P, Falk RJ, Jennette JC

Kidney diseases (Basel, Switzerland) 2016; (1(4)):205-15 doi:10.1159/000442323.

[Pulmonar pseudotumor in granulomatosis with polyangiitis (GPA). Pulmonary cancer and/or GPA? Diagnostic implications of pulmonary nodules].

Horta-Baas G, Meza-Zempoaltecatl E, Pérez-Cristóbal M, Barile-Fabris LA

Gaceta medica de Mexico 2016; (152(4)):521-8.

ANCA-associated vasculitis.

Yates M, Watts R

Clinical medicine (London, England) 2017; (17(1)):60-64 doi:10.7861/clinmedicine.17-1-60.

An overlap of granulomatosis with polyangiitis and eosinophilic granulomatosis with polyangiitis.

Surendran S, Gundappa C, Gandhi A, et al.

Saudi journal of kidney diseases and transplantation : an official publication of the Saudi Center for Organ Transplantation, Saudi Arabia 2017; (28(3)):639-644 doi:10.4103/1319-2442.206450.

ANCA-associated vasculitis with renal involvement.

Binda V, Moroni G, Messa P

Journal of nephrology 2018; (31(2)):197-208 doi:10.1007/s40620-017-0412-z.

Granulomatosis with Polyangiitis with Myocarditis and Ventricular Tachycardia.

Hanna RM, Lopez E, Wilson J

Case reports in medicine 2017; (2017()):6501738 doi:10.1155/2017/6501738.

Methotrexate versus cyclophosphamide for remission maintenance in ANCA-associated vasculitis: A randomised trial.

Maritati F, Alberici F, Oliva E, et al.

PloS one 2017; (12(10)):e0185880 doi:10.1371/journal.pone.0185880.

Relapsing granulomatosis with polyangiitis with severe lung and upper respiratory tract involvement successfully treated with rituximab.

Masiak A, Zdrojewski Z

Reumatologia 2017; (55(4)):208-212 doi:10.5114/reum.2017.69783.

Anti-neutrophil cytoplasmic antibodies and their clinical significance.

Suwanchote S, Rachayon M, Rodsaward P, et al.

Clinical rheumatology 2018; (37(4)):875-884 doi:10.1007/s10067-018-4062-x.

Delta Neutrophil Index Is Associated with Vasculitis Activity and Risk of Relapse in ANCA-Associated Vasculitis.

Yoo J, Ahn SS, Jung SM, et al.

Yonsei medical journal 2018; (59(3)):397-405 doi:10.3349/ymj.2018.59.3.397.

A clinical threat in patients with granulomatosis polyangiitis in remission: Subglottic stenosis.

Ugan Y, Doğru A, Aynalı G, et al.

European journal of rheumatology 2018; (5(1)):69-71 doi:10.5152/eurjrheum.2017.16025.

Severe localised granulomatosis with polyangiitis (Wegener's granulomatosis) manifesting with extensive cranial nerve palsies and cranial diabetes insipidus: a case report and literature review.

Peters JE, Gupta V, Saeed IT, et al.

BMC neurology 2018; (18(1)):59 doi:10.1186/s12883-018-1058-8.

Targeted immunotherapy strategies in ANCA-associated vasculitis.

Puéchal X

Joint bone spine 2019; (86(3)):321-326 doi:10.1016/j.jbspin.2018.09.002.

Granulomatosis with Polyangiitis (Wegener's Granulomatosis): Evolving Concepts in Treatment.

Lynch JP, Derhovanessian A, Tazelaar H, Belperio JA

Seminars in respiratory and critical care medicine 2018; (39(4)):434-458 doi:10.1055/s-0038-1660874.

A rare case report of polyangiitis overlap syndrome: granulomatosis with polyangiitis and eosinophilic granulomatosis with polyangiitis.

Quan MV, Frankel SK, Maleki-Fischbach M, Tan LD

BMC pulmonary medicine 2018; (18(1)):181 doi:10.1186/s12890-018-0733-2.

Anti-Neutrophil Cytoplasmic Antibody (ANCA) Associated Vasculitis Causes Aortic Valve Degeneration and Severe Aortic Regurgitation.

Guterbaum TJ, Husic M, Voss A, Dahl JS

The American journal of case reports 2019; (20()):423-429 doi:10.12659/AJCR.912693.

18F-Fluorodeoxyglucose Positron Emission Tomography/Computed Tomography in the Assessment of Occult Involvement in Widespread Granulomatosis with Polyangiitis (Wegener's Granulomatosis).

Saleh Farghaly HR, Alqarni AO, Nasr HA

Indian journal of nuclear medicine : IJNM : the official journal of the Society of Nuclear Medicine, India 2019; (34(2)):153-156 doi:10.4103/ijnm.IJNM_151_18.

Risk factors for cytomegalovirus infection in patients with antineutrophil cytoplasmic antibody-associated vasculitis.

Morishita M, Sada KE, Matsumoto Y, et al.

PloS one 2019; (14(7)):e0218705 doi:10.1371/journal.pone.0218705.

ANCA-Associated Vasculitis: Core Curriculum 2020.

Geetha D, Jefferson JA

American journal of kidney diseases : the official journal of the National Kidney Foundation 2020; (75(1)):124-137 doi:10.1053/j.ajkd.2019.04.031.

Remission maintenance in ANCA-associated vasculitis: does one size fit all?

Berti A, Specks U

Expert review of clinical immunology 2019; (15(12)):1273-1286 doi:10.1080/1744666X.2020.1693260.

Measuring Vasculitis with Numbers: Outcome Scores.

Batu ED, Ozen S

Current rheumatology reviews 2020; (16(1)):21-28 doi:10.2174/1573397115666191126093927.

Elevated levels of d-dimer are associated with inflammation and disease activity rather than risk of venous thromboembolism in patients with granulomatosis with polyangiitis in long term observation.

Borowiec A, Dąbrowski R, Kowalik I, et al.

Advances in medical sciences 2020; (65(1)):97-101 doi:10.1016/j.advms.2019.12.007.

Monitoring the activity of anca-associated vasculitis: some questionnaires and laboratory parameters

Suszek D, Majdan M, Widłak K, et al.

Wiadomosci lekarskie (Warsaw, Poland : 1960) 2019; (72(10)):2010-2016.

Therapeutic Complement Targeting in ANCA-Associated Vasculitides and Thrombotic Microangiopathy.

Novikov P, Kozlovskaya N, Moiseev S, et al.

Biomedicine hub 2016; (1(3)):1-11 doi:10.1159/000453106.

High incidence of venous thromboembolism but not of coronary artery disease in granulomatosis with polyangiitis in first years after diagnosis.

Borowiec A, Hadzik-Błaszczyk M, Kowalik I, et al.

Sarcoidosis, vasculitis, and diffuse lung diseases : official journal of WASOG 2019; (36(3)):202-208 doi:10.36141/svdld.v36i3.8088.

Abdominal Pain, an Atypical Presenting Symptom of Granulomatosis with Polyangiitis.

Desai K, Jose M, Ogbebor O

Cureus 2020; (12(4)):e7864 doi:10.7759/cureus.7864.

How to improve the histopathological diagnosis of systemic vasculitides in daily practice?

Honsová E

Ceskoslovenska patologie 2020; (56(2)):68-73.

Localized Granulomatous with Polyangiitis (GPA): Varied Clinical Presentations and Update on Treatment.

Sattui SE, Lally L

Current allergy and asthma reports 2020; (20(10)):56 doi:10.1007/s11882-020-00953-1.

New lung mass in a patient with granulomatosis with polyangiitis.

Masiak A, Fijałkowska J, Nowakowski S, et al.

Rheumatology international 2021; (41(2)):493-499 doi:10.1007/s00296-020-04646-w.

Plasma exchange for the management of ANCA-associated vasculitis: the con position.

Specks U, Fussner LA, Cartin-Ceba R, et al.

Nephrology, dialysis, transplantation : official publication of the European Dialysis and Transplant Association - European Renal Association 2021; (36(2)):231-236 doi:10.1093/ndt/gfaa312.

Plasma exchange in ANCA-associated vasculitis: the pro position.

Kronbichler A, Shin JI, Wang CS, et al.

Nephrology, dialysis, transplantation : official publication of the European Dialysis and Transplant Association - European Renal Association 2021; (36(2)):227-231 doi:10.1093/ndt/gfaa311.

[Cortisone-free rheumatology-Vasculitides].

Holle JU, Moosig F

Zeitschrift fur Rheumatologie 2021; (80(4)):314-321 doi:10.1007/s00393-021-00974-9.

Association Between Serum Alarmin Levels and Disease-specific Indices in Patients With Anti-neutrophil Cytoplasmic Antibody-associated Vasculitis.

Ahn SS, Yoon T, Song JJ, et al.

In vivo (Athens, Greece) 2021; (35(3)):1761-1768 doi:10.21873/invivo.12435.

Granulomatosis with Polyangiitis: Recurrence or Treatment Consequences?

Diegues A, Tavares J, Sá D, et al.

European journal of case reports in internal medicine 2021; (8(4)):002448 doi:10.12890/2021_002448.

Tumor-like Lesions in Patients with Granulomatosis with Polyangiitis: A Case Series.

Gendelman O, Kuntzman Y, Shovman O, et al.

The Israel Medical Association journal : IMAJ 2021; (23(6)):350-352.

Granulomatous Inflammation in ANCA-Associated Vasculitis.

Müller A, Krause B, Kerstein-Stähle A, et al.

International journal of molecular sciences 2021; (22(12)) doi:10.3390/ijms22126474.

Consideration of Therapeutic Plasma Exchange in Association With Inflammatory Lesions in ANCA-Associated Glomerulonephritis: A Real-World Retrospective Study From a Single Center.

Tampe D, Ströbel P, Korsten P, et al.

Frontiers in immunology 2021; (12()):645483 doi:10.3389/fimmu.2021.645483.

Granulomatosis with polyangiitis: A case report and brief review of literature.

Lakhani DA, Balar AB, Adelanwa A, et al.

Radiology case reports 2021; (16(11)):3445-3450 doi:10.1016/j.radcr.2021.08.028.

Epidemiology and genetics of granulomatosis with polyangiitis.

Banerjee P, Jain A, Kumar U, Senapati S

Rheumatology international 2021; (41(12)):2069-2089 doi:10.1007/s00296-021-05011-1.

Plasma Exchange in ANCA-Associated Vasculitis: A Narrative Review.

Tsiakas S, Marinaki S, Lionaki S, Boletis J

Journal of clinical medicine 2021; (10(21)) doi:10.3390/jcm10215154.

Avacopan: First Approval.

Lee A

Drugs 2022; (82(1)):79-85 doi:10.1007/s40265-021-01643-6.

Association of antineutrophil cytoplasmic antibody (ANCA) specificity with demographic and clinical characteristics of patients with ANCA‑associated vasculitides.

Wójcik K, Masiak A, Jeleniewicz R, et al.

Polish archives of internal medicine 2022; (132(3)) doi:10.20452/pamw.16187.

ANCA-Associated Vasculitic Neuropathies: A Review.

Koike H, Nishi R, Ohyama K, et al.

Neurology and therapy 2022; (11(1)):21-38 doi:10.1007/s40120-021-00315-7.

[Update on etiopathogenesis of small vessel vasculitis].

Arnold S, Holl-Ulrich K, Müller A, et al.

Zeitschrift fur Rheumatologie 2022; (81(4)):270-279 doi:10.1007/s00393-021-01155-4.

Recent Advancements in the Management of Anti-neutrophil Cytoplasmic Antibody-Associated Vasculitis: A Systematic Review.

Arzoun H, Srinivasan M, Thangaraj SR, et al.

Cureus 2022; (14(2)):e21814 doi:10.7759/cureus.21814.

Antineutrophil cytoplasmic antibody-negative granulomatosis with polyangiitis localized to the lungs.

Ohteru Y, Hamada K, Oishi K, et al.

Respiratory medicine case reports 2022; (36()):101600 doi:10.1016/j.rmcr.2022.101600.

A Rare Case of Nephrotic-Range Proteinuria in Antineutrophil Cytoplasmic Antibodies (ANCA)-Associated Vasculitis.

Nasr R, Balasubramanian P, Desiderio L, Abdelattif M

Cureus 2022; (14(5)):e24889 doi:10.7759/cureus.24889.

[ANCA-Associated Vasculitides].

Stegert M, Neumann T, Daikeler T

Therapeutische Umschau. Revue therapeutique 2022; (79(5)):229-237 doi:10.1024/0040-5930/a001355.

Serum B cell activating factor (BAFF) as a biomarker for induction of remission with rituximab in ANCA-associated vasculitis.

Tsuboi K, Noguchi K, Kitano M, et al.

Immunological medicine 2022; (45(4)):238-243 doi:10.1080/25785826.2022.2094592.

ANCA associated vasculitis (AAV): a review for internists.

Yaseen K, Mandell BF

Postgraduate medicine 2023; (135(sup1)):3-13 doi:10.1080/00325481.2022.2102368.

Migrant cavitation as primary involvement in a particular case of granulomatosis with polyangiitis.

Manti F, Battaglia C, Pelaia C, et al.

Radiology case reports 2022; (17(10)):3535-3538 doi:10.1016/j.radcr.2022.06.074.

[ANCA-associated vasculitis].

Krasselt ML, Holle JU

Innere Medizin (Heidelberg, Germany) 2022; (63(9)):947-960 doi:10.1007/s00108-022-01386-w.

[Granulomatous vasculitides and vasculitides with extravascular granulomatosis].

Arnold S, Klapa S, Holl-Ulrich K, et al.

Zeitschrift fur Rheumatologie 2022; (81(7)):558-566 doi:10.1007/s00393-022-01249-7.

Neutrophils in ANCA-associated vasculitis: Mechanisms and implications for management.

Ge S, Zhu X, Xu Q, et al.

Frontiers in pharmacology 2022; (13()):957660 doi:10.3389/fphar.2022.957660.

Type of ANCA May Be Indispensable in Distinguishing Subphenotypes of Different Clinical Entities in ANCA-Associated Vasculitis.

Konstantouli AM, Lioulios G, Stai S, et al.

Life (Basel, Switzerland) 2022; (12(10)) doi:10.3390/life12101467.

Granulomatosis With Polyangiitis: A Clinical Case.

Rodrigues F, Oliveira Sá AI, Mendes M, et al.

Cureus 2022; (14(12)):e32410 doi:10.7759/cureus.32410.

Oral manifestations of anti-neutrophil cytoplasmic antibody-associated vasculitis: an update and narrative review of the literature.

Alamoudi WA, Sollecito TP, Stoopler ET, France K

Oral surgery, oral medicine, oral pathology and oral radiology 2023; (135(3)):372-384 doi:10.1016/j.oooo.2022.11.013.

An update on dıagnosıs and treatment of ANCA assocıated renal vasculıtıs.

Turkmen K, Ozer H, Tesar V

International urology and nephrology 2023; (55(11)):2817-2827 doi:10.1007/s11255-023-03565-6.

A Runny Nose Leads to a Rare Diagnosis: Chronic Sinusitis as a Sole Manifestation of Limited Granulomatosis With Polyangiitis.

Qudsiya Z, Viqas Z, Baker DL

Cureus 2023; (15(5)):e39203 doi:10.7759/cureus.39203.

[Pharmacological and clinical profiles of avacopan (TAVNEOS® capsule), a selective C5a receptor antagonist].

Maruyama Y, Yoshida T, Maruyama I

Nihon yakurigaku zasshi. Folia pharmacologica Japonica 2023; (158(5)):399-407 doi:10.1254/fpj.22161.

Subglottic Stenosis as a Presentation of Antineutrophil Cytoplasmic Antibody-Associated Glomerulonephritis.

Patrick Eisenberg A, Collier V, Mangano A, et al.

Cureus 2023; (15(10)):e46899 doi:10.7759/cureus.46899.

Diagnosis and management of facial nerve palsy secondary to granulomatosis with polyangiitis - A systematic review.

Odom JQ, Mangan AR, Gibson AC, et al.

American journal of otolaryngology 2024; (45(2)):104132 doi:10.1016/j.amjoto.2023.104132.

[Granulomatosis with polyangiitis and microscopic polyangiitis].

Klapa S, Arnold S, Lamprecht P

Laryngo- rhino- otologie 2024; (103(7)):490-499 doi:10.1055/a-2217-4457.

Diagnosis and management of ANCA-associated vasculitis.

Kronbichler A, Bajema IM, Bruchfeld A, et al.

Lancet (London, England) 2024; (403(10427)):683-698 doi:10.1016/S0140-6736(23)01736-1.

A Rare Case of Granulomatosis With Polyangiitis Complicated by Splenic Rupture.

Awad OM, Srour IA, Mekdad FA, et al.

Cureus 2024; (16(1)):e52536 doi:10.7759/cureus.52536.

Proteinase 3-specific antineutrophil cytoplasmic antibody-associated vasculitis.

Falde SD, Fussner LA, Tazelaar HD, et al.

The Lancet. Rheumatology 2024; (6(5)):e314-e327 doi:10.1016/S2665-9913(24)00035-3.

Granulomatosis With Polyangiitis: Cardiac, Renal, and Respiratory Involvement.

Khatiwala P, Patel P, Nachodsky A

Cureus 2024; (16(6)):e61529 doi:10.7759/cureus.61529.

Ocular manifestations in ANCA-associated vasculitis: a comprehensive analysis from Chinese medical centers.

Liu S, Xu M, Zhao X, et al.

Clinical rheumatology 2024; (43(9)):2899-2910 doi:10.1007/s10067-024-07034-y.

Dacryoadenitis: do not forget ANCA vasculitis.

Derbel A, Salah RB, Boukhzar R, et al.

Romanian journal of ophthalmology 2024; (68(2)):187-190 doi:10.22336/rjo.2024.35.

Update on targeted treatments for ANCA-associated vasculitis.

Puéchal X

Joint bone spine 2025; (92(1)):105768 doi:10.1016/j.jbspin.2024.105768.

Undisclosed facts in Friedrich Wegener's links with Nazism.

Arkuszewski P, Cieślak-Arkuszewska A

Histopathology 2025; (86(3)):317-326 doi:10.1111/his.15296.

Superiority of Avacopan and Mepolizumab to Glucocorticoid Tapering in the Treatment of Anti-neutrophil Cytoplasmic Antibody (ANCA)-Associated Vasculitis: A Systematic Review.

Gattu R, Demory Beckler M, Kesselman MM

Cureus 2024; (16(8)):e67161 doi:10.7759/cureus.67161.

Granulomatosis With Polyangiitis Misdiagnosed as Tuberculosis: A Case Report.

Martins JD, Soares C, Barreiros C, et al.

Cureus 2024; (16(10)):e71834 doi:10.7759/cureus.71834.

Granulomatosis with Polyangiitis: A Focus on Differences and Similarities Between Child and Adult Patients.

Calabrese V, Gallizzi R, Spagnolo A, et al.

Medicina (Kaunas, Lithuania) 2025; (61(3)) doi:10.3390/medicina61030534.

Thoracic Manifestations of ANCA-associated Vasculitis: Review of the 2022 American College of Rheumatology-European Alliance of Associations of Rheumatology Classification Criteria.

Kwon J, Choi YW, Kim H, Yoo SJ

Radiographics : a review publication of the Radiological Society of North America, Inc 2025; (45(4)):e240089 doi:10.1148/rg.240089.

Laryngeal Frame Involvement as The First Sign of Wegener's Granulomatosis.

Burrascano D, Verro B, Ottoveggio G, et al.

Iranian journal of otorhinolaryngology 2025; (37(2)):95-98 doi:10.22038/ijorl.2024.81617.3746.

Safety of Avacopan for the Treatment of Antineutrophil Cytoplasmic Antibody-Associated Vasculitis: Combined Data From Three Clinical Trials.

Merkel PA, George MD, Yue H, et al.

ACR open rheumatology 2025; (7(4)):e70001 doi:10.1002/acr2.70001.

Drug-induced liver injury due to avacopan improved by mycophenolate mofetil: A case report.

Yamashita R, Izumi Y, Takane K, et al.

Medicine 2025; (104(15)):e42121 doi:10.1097/MD.0000000000042121.

A Rare Case of Granulomatosis With Polyangiitis With Cutaneous Pyoderma Gangrenosum-Like Lesions of the Bilateral Parotid Glands.

Short SH, McGlone M, Ohlstein JF

Ear, nose, & throat journal 2025; 1455613251345431 doi:10.1177/01455613251345431.

[How do I treat ANCA vasculitis with renal involvement].

Crucil M, Regnier C, Von Frenckell C, et al.

Revue medicale de Liege 2025; (80(9)):556-562.

Mapping a path forward: addressing disease burden, pathways and solutions in ANCA-associated vasculitis.

Hellmich B

Rheumatology (Oxford, England) 2026; (65(Supplement_1)):i1-i5 doi:10.1093/rheumatology/keaf517.

Efficacy and safety of avacopan for treatment of patients with ANCA-associated vasculitis receiving cyclophosphamide.

Geetha D, Neumann T, Karras A, et al.

RMD open 2025; (11(4)) doi:10.1136/rmdopen-2025-005743.

ANCA-negative Pauci-immune Vasculitis, an Often-missed Clinical Entity: A Case Report.

Tudu A, Paul S, Ghosh UC, Banerjee B

The Journal of the Association of Physicians of India 2025; (73(11S)):40-42 doi:10.59556/japi.73.1245.

Granulomatosis With Polyangiitis (Wegener Granulomatosis): Then and Now.

Churg A, Muller NL

Archives of pathology & laboratory medicine 2025; (150(1)):37-43 doi:10.5858/arpa.2025-0146-RA.

Expanding the Role of Avacopan Beyond Renal Involvement: Clinical Insights from Two Cases.

Henriques AR, Oliveira N, Castro P, et al.

Modern rheumatology case reports 2026; doi:10.1093/mrcr/rxag022.