Research & Literature

Long-Term Followup of a Multicenter Cohort of 101 Patients With Eosinophilic Granulomatosis With Polyangiitis (Churg-Strauss).

Durel CA, Berthiller J, Caboni S, et al.

Arthritis care & research 2016; (68(3)):374-87 doi:10.1002/acr.22686.

Otologic and Rhinologic Manifestations of Eosinophilic Granulomatosis with Polyangiitis.

Nakamaru Y, Takagi D, Suzuki M, et al.

Audiology & neuro-otology 2016; (21(1)):45-53 doi:10.1159/000442040.

[Clinical analysis of 43 patients with eosinophilic granulomatosis with polyangiitis].

Li J, Zhang L, Zhao W, et al.

Zhonghua yi xue za zhi 2016; (96(10)):787-91 doi:10.3760/cma.j.issn.0376-2491.2016.10.008.

Mepolizumab or Placebo for Eosinophilic Granulomatosis with Polyangiitis.

Wechsler ME, Akuthota P, Jayne D, et al.

The New England journal of medicine 2017; (376(20)):1921-1932 doi:10.1056/NEJMoa1702079.

The Epidemiology of Antineutrophil Cytoplasmic Autoantibody-Associated Vasculitis in Olmsted County, Minnesota: A Twenty-Year US Population-Based Study.

Berti A, Cornec D, Crowson CS, et al.

Arthritis & rheumatology (Hoboken, N.J.) 2017; (69(12)):2338-2350 doi:10.1002/art.40313.

[Eosinophilic granulomatosis with polyangiitis (Churg-Strauss syndrome)].

Jerrentrup A, Müller T, Mariss J, Dylla S

Der Internist 2018; (59(5)):497-504 doi:10.1007/s00108-017-0303-3.

Clinical and Serological Features of Eosinophilic and Vasculitic Phases of Eosinophilic Granulomatosis with Poliangiitis: a Case Series of 15 Patients.

Yılmaz İ, Tutar N, Şimşek ZÖ, et al.

Turkish thoracic journal 2017; (18(3)):72-77 doi:10.5152/TurkThoracJ.2017.16040.

Churg-Strauss Syndrome or Eosinophilic Granulomatosis with Polyangiitis: Exuberant Classic Clinical Picture of a Rare Disease.

Mukamal LV, Sodré CT, Prata LB, et al.

Case reports in dermatology 2018; (10(2)):175-181 doi:10.1159/000489162.

A rare case of eosinophilic granulomatosis with polyangiitis complicated with progressive pericardial effusion.

Arinaga T, Komaki T, Miura SI, et al.

Journal of cardiology cases 2017; (15(5)):163-166 doi:10.1016/j.jccase.2017.01.001.

Eosinophilic Granulomatosis with Polyangiitis (Churg-Strauss).

Nguyen Y, Guillevin L

Seminars in respiratory and critical care medicine 2018; (39(4)):471-481 doi:10.1055/s-0038-1669454.

Refractory diffuse alveolar hemorrhage caused by eosinophilic granulomatosis with polyangiitis in the absence of elevated biomarkers treated successfully by rituximab and mepolizumab: A case report.

Shiroshita A, Nakashima K, Motojima S, Aoshima M

Respiratory medicine case reports 2019; (26()):112-114 doi:10.1016/j.rmcr.2018.12.010.

Comparison of the Birmingham Vasculitis Activity Score and the Five-Factor Score to Assess Survival in Antineutrophil Cytoplasmic Antibody-Associated Vasculitis: A Study of 550 Patients From Spain (REVAS Registry).

Solans-Laqué R, Rodriguez-Carballeira M, Rios-Blanco JJ, et al.

Arthritis care & research 2020; (72(7)):1001-1010 doi:10.1002/acr.23912.

Genome-wide association study of eosinophilic granulomatosis with polyangiitis reveals genomic loci stratified by ANCA status.

Lyons PA, Peters JE, Alberici F, et al.

Nature communications 2019; (10(1)):5120 doi:10.1038/s41467-019-12515-9.

Severe mononeuritis multiplex in a patient with eosinophilic granulomatosis with polyangiitis.

Kalinova D, Kukushev G, Kolarov Z, Rashkov R

Reumatologia 2019; (57(5)):288-291 doi:10.5114/reum.2019.89522.

Differential clinicopathologic features of EGPA-associated neuropathy with and without ANCA.

Nishi R, Koike H, Ohyama K, et al.

Neurology 2020; (94(16)):e1726-e1737 doi:10.1212/WNL.0000000000009309.

Utility of the Brief Illness Perception Questionnaire to Monitor Patient Beliefs in Systemic Vasculitis.

Schwartz MN, Rimland CA, Quinn KA, et al.

The Journal of rheumatology 2020; (47(12)):1785-1792 doi:10.3899/jrheum.190828.

Definite IgG4-related disease had no overlap with eosinophilic granulomatosis with polyangiitis in Korean patients: a pilot study in one centre.

Yoo J, Song JJ, Park YB, Lee SW

Clinical rheumatology 2020; (39(10)):3009-3015 doi:10.1007/s10067-020-05104-5.

Granulomatosis with polyangiitis (Wegener's).

Puéchal X

Joint bone spine 2020; (87(6)):572-578 doi:10.1016/j.jbspin.2020.06.005.

Updates for the treatment of EGPA.

Raffray L, Guillevin L

Presse medicale (Paris, France : 1983) 2020; (49(3)):104036 doi:10.1016/j.lpm.2020.104036.

The role of surgery in antineutrophil cytoplasmic antibody-associated vasculitides affecting the nose and sinuses: A systematic review.

Pendolino AL, Unadkat S, Zhang H, et al.

SAGE open medicine 2020; (8()):2050312120936731 doi:10.1177/2050312120936731.

Antineutrophil Cytoplasmic Antibodies and Organ-Specific Manifestations in Eosinophilic Granulomatosis with Polyangiitis: A Systematic Review and Meta-Analysis.

Chang HC, Chou PC, Lai CY, Tsai HH

The journal of allergy and clinical immunology. In practice 2021; (9(1)):445-452.e6 doi:10.1016/j.jaip.2020.07.038.

Renal involvement in eosinophilic granulomatosis with polyangiitis (EGPA): a multicentric retrospective study of 63 biopsy-proven cases.

Durel CA, Sinico RA, Teixeira V, et al.

Rheumatology (Oxford, England) 2021; (60(1)):359-365 doi:10.1093/rheumatology/keaa416.

[A Rare Cause of a Eosinophilic Lung Disease].

Stolpe C, Tannapfel A

Pneumologie (Stuttgart, Germany) 2021; (75(3)):221-225 doi:10.1055/a-1220-7149.

A new index for distinguishing hypereosinophilic syndrome and antineutrophil cytoplasmic antibody-negative eosinophilic granulomatosis with polyangiitis.

Ahn SS, Yoo J, Park YB, et al.

Asian Pacific journal of allergy and immunology 2023; (41(3)):244-252 doi:10.12932/AP-080420-0805.

Significance of PR3-ANCA positivity in eosinophilic granulomatosis with polyangiitis (Churg-Strauss).

Papo M, Sinico RA, Teixeira V, et al.

Rheumatology (Oxford, England) 2021; (60(9)):4355-4360 doi:10.1093/rheumatology/keaa805.

Cardiac Eosinophilic Masses in Man With Eosinophilic Granulomatosis With Polyangiitis.

Amidi O, Siebert VRJ, Allison J, Hamzeh IR

Texas Heart Institute journal 2020; (47(4)):337-338 doi:10.14503/THIJ-19-7084.

The First Case of Eosinophilic Granulomatosis with Polyangiitis Simultaneously Demonstrating Various Clinical Manifestations with Retroperitoneal Fibrosis and Membranous Nephropathy.

Kondo I, Arai Y, Sakamoto E, et al.

Internal medicine (Tokyo, Japan) 2021; (60(12)):1963-1969 doi:10.2169/internalmedicine.6399-20.

Otologic Manifestations of Eosinophilic Granulomatosis With Polyangiitis: A Systematic Review.

Ashman PE, Chen T, Barinsky GL, et al.

Otology & neurotology : official publication of the American Otological Society, American Neurotology Society [and] European Academy of Otology and Neurotology 2021; (42(4)):e380-e387 doi:10.1097/MAO.0000000000003024.

Cardiac manifestations of eosinophilic granulomatosis with polyangiitis from a single-center cohort in China: clinical features and associated factors.

Liu S, Guo L, Zhang Z, et al.

Therapeutic advances in chronic disease 2021; (12()):2040622320987051 doi:10.1177/2040622320987051.

Eosinophilic Granulomatosis With Polyangiitis: Dissecting the Pathophysiology.

Fagni F, Bello F, Emmi G

Frontiers in medicine 2021; (8()):627776 doi:10.3389/fmed.2021.627776.

Eosinophilic Granulomatosis with Polyangiitis Presenting with Central Retinal Artery Occlusion During Treatment with Anti-interleukin-5 Receptor Monoclonal Antibody.

Nishiyama H, Tajiri T, Yamabe T, et al.

Internal medicine (Tokyo, Japan) 2021; (60(22)):3631-3634 doi:10.2169/internalmedicine.7027-21.

2021 American College of Rheumatology/Vasculitis Foundation Guideline for the Management of Antineutrophil Cytoplasmic Antibody-Associated Vasculitis.

Chung SA, Langford CA, Maz M, et al.

Arthritis care & research 2021; (73(8)):1088-1105 doi:10.1002/acr.24634.

2021 American College of Rheumatology/Vasculitis Foundation Guideline for the Management of Antineutrophil Cytoplasmic Antibody-Associated Vasculitis.

Chung SA, Langford CA, Maz M, et al.

Arthritis & rheumatology (Hoboken, N.J.) 2021; (73(8)):1366-1383 doi:10.1002/art.41773.

Pathological findings of hypertrophic pachymeningitis associated with eosinophilic granulomatosis with polyangiitis.

Shiraishi W, Tsujimoto Y, Shiraishi T

BMJ case reports 2021; (14(9)) doi:10.1136/bcr-2021-243395.

2022 American College of Rheumatology/European Alliance of Associations for Rheumatology Classification Criteria for Eosinophilic Granulomatosis With Polyangiitis.

Grayson PC, Ponte C, Suppiah R, et al.

Arthritis & rheumatology (Hoboken, N.J.) 2022; (74(3)):386-392 doi:10.1002/art.41982.

2022 American College of Rheumatology/European Alliance of Associations for Rheumatology Classification Criteria for Eosinophilic Granulomatosis with Polyangiitis.

Grayson PC, Ponte C, Suppiah R, et al.

Annals of the rheumatic diseases 2022; (81(3)):309-314 doi:10.1136/annrheumdis-2021-221794.

[ANCA-associated small-vessel vasculitides].

Bayrashevskaya AV, Degtyareva ND, Radenska-Lopovok SG

Arkhiv patologii 2022; (84(1)):50-58 doi:10.17116/patol20228401150.

Hypertrophic Pachymeningitis Development in Eosinophilic Granulomatosis with Polyangiitis at Relapse of Disease: A Case-Based Review.

Kiyohara M, Shirai T, Nishiyama S, et al.

The Tohoku journal of experimental medicine 2022; (256(3)):241-247 doi:10.1620/tjem.256.241.

A Case of Eosinophilic Granulomatosis with Polyangiitis Presenting with Mononeuritis Multiplex.

Alam MA, Hossain MI, Khan AH, Arafat SM

Current rheumatology reviews 2022; (18(4)):368-372 doi:10.2174/1573397118666220330005431.

In vivo visualization of eosinophil secretion in eosinophilic granulomatosis with polyangiitis: An ultrastructural study.

Koike H, Nishi R, Furukawa S, et al.

Allergology international : official journal of the Japanese Society of Allergology 2022; (71(3)):373-382 doi:10.1016/j.alit.2022.02.009.

ANCA-associated vasculitis and IgG4-related disease overlap syndrome: a case report and literature review.

Faz-Muñoz D, Hinojosa-Azaola A, Mejía-Vilet JM, et al.

Immunologic research 2022; (70(4)):550-559 doi:10.1007/s12026-022-09279-8.

Case Report: An Unusual Presentation of Cardiovascular Involvement in Eosinophilic Granulomatosis With Polyangiitis.

Li Y, Zhou H, Zhou Y, Tang H

Frontiers in cardiovascular medicine 2022; (9()):928192 doi:10.3389/fcvm.2022.928192.

Severe eosinophilic granulomatosis with polyangiitis responding to a combination of rituximab and mepolizumab.

Tsioulos G, Kounatidis D, Vallianou NG, et al.

The American journal of the medical sciences 2023; (365(1)):93-98 doi:10.1016/j.amjms.2022.07.007.

Glomerulonephritis and Interstitial Nephritis Originating from Vasculitis of the Interlobular Arteries of the Kidney in a Patient with Eosinophilic Granulomatosis with Polyangiitis.

Nawata T, Shibuya M, Takeshita Y, et al.

Case reports in rheumatology 2022; (2022()):9606981 doi:10.1155/2022/9606981.

Clinical characteristics and long-term outcome of patients with gastrointestinal involvement in eosinophilic granulomatosis with polyangiitis.

Li R, Chen Y, Zhang S, et al.

Frontiers in immunology 2022; (13()):1099722 doi:10.3389/fimmu.2022.1099722.

[Eosinophilic granulomatosis with polyangiitis].

Romero Gómez C, Hernández Negrín H, Ayala Gutiérrez MDM

Medicina clinica 2023; (160(7)):310-317 doi:10.1016/j.medcli.2023.01.003.

Eosinophilic granulomatosis with polyangiitis: case report and literature review.

Alam V, Nanzer AM

Breathe (Sheffield, England) 2022; (18(4)):220170 doi:10.1183/20734735.0170-2022.

EULAR recommendations for the management of ANCA-associated vasculitis: 2022 update.

Hellmich B, Sanchez-Alamo B, Schirmer JH, et al.

Annals of the rheumatic diseases 2024; (83(1)):30-47 doi:10.1136/ard-2022-223764.

Retrospective Analysis of the Burden of Illness of Eosinophilic Granulomatosis With Polyangiitis (EGPA) Versus Asthma in Commercially Insured US Patients.

Bell CF, Ajmera M, Meyers J

Cureus 2023; (15(7)):e42241 doi:10.7759/cureus.42241.

ANCA-negative EGPA: only eosinophils without vasculitis? Insights from anti-T2 biologics.

Piga MA, Fraticelli P, Antonicelli L, et al.

Frontiers in immunology 2023; (14()):1325299 doi:10.3389/fimmu.2023.1325299.

Clinical implications of peripheral eosinophil count at diagnosis in patients newly diagnosed with microscopic polyangiitis and granulomatosis with polyangiitis.

Ha JW, Ahn SS, Song JJ, et al.

Arthritis research & therapy 2023; (25(1)):245 doi:10.1186/s13075-023-03233-1.

Eosinophilic granulomatosis with polyangiitis: sequential use of mepolizumab following rituximab for inadequate asthma control despite vasculitis remission.

Cremonezi Lammoglia B, De Aguiar Trevise L, Paslar Leal T, et al.

Reumatismo 2023; (75(4)) doi:10.4081/reumatismo.2023.1588.

When inflammation is not just inflammation-A review of systemic diseases of the nose and sinuses part 2: Granulomatosis with polyangiitis and eosinophilic granulomatosis with polyangiitis.

Cler SJ, Ogden MA, Farrell NF, et al.

American journal of otolaryngology 2024; (45(3)):104207 doi:10.1016/j.amjoto.2023.104207.

Incidence, Prevalence, and Mortality of Eosinophilic Granulomatosis With Polyangiitis in Korea: A Nationwide Population-Based Study.

Lee JH, Hong SH, Yu I, et al.

Allergy, asthma & immunology research 2024; (16(2)):168-178 doi:10.4168/aair.2024.16.2.168.

Clinical Characteristics of EGPA Patients in Comparison to GPA Subgroup with Increased Blood Eosinophilia from POLVAS Registry.

Drynda A, Padjas A, Wójcik K, et al.

Journal of immunology research 2024; (2024()):4283928 doi:10.1155/2024/4283928.

Severe heart failure and intracardiac thrombosis: going beyond the appearance for diagnosis and treatments.

Segreti A, Mastroberardino S, Frau L, et al.

Monaldi archives for chest disease = Archivio Monaldi per le malattie del torace 2025; (95(2)) doi:10.4081/monaldi.2024.2882.

Prevalence, incidence and healthcare burden of eosinophilic granulomatosis with polyangiitis in the UK.

Hwee J, Harper L, Fu Q, et al.

ERJ open research 2024; (10(3)) doi:10.1183/23120541.00430-2023.

Hypertrophic Pachymeningitis, Associated with Eosinophilic Granulomatosis with Polyangiitis, and ANCA-Negative Serology.

Martínez-Piña DA, Calderón-Garcidueñas AL, Gama-Lizárraga E, et al.

European journal of case reports in internal medicine 2024; (11(7)):004595 doi:10.12890/2024_004595.

Genetic and Non-Genetic Contributions to Eosinophilic Granulomatosis with Polyangiitis: Current Knowledge and Future Perspectives.

Treccani M, Veschetti L, Patuzzo C, et al.

Current issues in molecular biology 2024; (46(7)):7516-7529 doi:10.3390/cimb46070446.

Looking Beyond Pneumonia and Asthma in India: An Interesting Case of Churg-Strauss Syndrome.

Kumar A, Gaba M, Kumar N, Kumar A

Cureus 2024; (16(8)):e66416 doi:10.7759/cureus.66416.

A discussion on a suspected case with EGPA after maintenance hemodialysis for 5 years and related literature analysis: A case report.

Zhao L, Zhang C

Medicine 2024; (103(38)):e39856 doi:10.1097/MD.0000000000039856.

Efficacy and Safety of Mepolizumab in Patients With Eosinophilic Granulomatosis With Polyangiitis: A Single-Center Experience.

Abuzakouk M, Isse S, Wechsler M, et al.

Cureus 2024; (16(8)):e68282 doi:10.7759/cureus.68282.

Real-world safety and effectiveness of mepolizumab for patients with eosinophilic granulomatosis with polyangiitis in Japan: Long-term observation of the MARS study.

Ishii T, Kunishige H, Kobayashi T, et al.

Modern rheumatology 2025; (35(3)):505-515 doi:10.1093/mr/roae100.

Real-world mepolizumab treatment in eosinophilic granulomatosis with polyangiitis reduces disease burden in the United States.

Mathur SK, Silver J, MacKnight SD, et al.

Annals of allergy, asthma & immunology : official publication of the American College of Allergy, Asthma, & Immunology 2025; (134(3)):341-350.e2 doi:10.1016/j.anai.2024.11.004.

Similarities and differences of clinical manifestations and prognosis between eosinophilic gastroenteritis and eosinophilic granulomatosis with polyangiitis complicating gastrointestinal involvement.

Li K, Jia Y, Ruan G, et al.

Clinical rheumatology 2025; (44(3)):1259-1268 doi:10.1007/s10067-024-07286-8.

The diagnosis of eosinophilic granulomatosis with polyangiitis has been 'masked' by asthma: a case report.

Xie H, Zhang X, Zhang J, et al.

AME case reports 2025; (9()):31 doi:10.21037/acr-24-79.

A Rare Case of Eosinophilic Granulomatosis with Polyangiitis Following Development of Central Diabetes Insipidus: A Case Report and Literature Review.

Kosaka T, Yamamoto S, Yasugi N, et al.

Internal medicine (Tokyo, Japan) 2026; (65(1)):149-155 doi:10.2169/internalmedicine.5558-25.

Unraveling cerebrovascular involvement in EGPA through digital subtraction angiography: case presentation and systematic literature review.

Vasandani V, O'Leary S, Gandhi R, et al.

BMC rheumatology 2025; (9(1)):80 doi:10.1186/s41927-025-00518-7.

Primary care physicians play a crucial role in diagnosing and managing rare eosinophilic diseases: HES and EGPA.

Shum M, Gewurz-Singer O, Silver J, Akuthota P

Frontiers in medicine 2025; (12()):1568770 doi:10.3389/fmed.2025.1568770.

Cardiac Involvement in Eosinophilic Granulomatosis with Polyangiitis.

Srikantharajah M, Gopalan D, Wilson-Morkeh H, et al.

Current cardiology reports 2025; (27(1)):109.

A Rare Presentation of Bilateral Foot Drop in Anti-neutrophil Cytoplasmic Antibody (ANCA)-Negative Eosinophilic Granulomatosis With Polyangiitis (Churg-Strauss Syndrome): A Diagnostic Challenge.

Isar MM, Al-Banna M, Hulo MG, et al.

Cureus 2025; (17(6)):e86765 doi:10.7759/cureus.86765.

A case of cardiac arrest and spontaneous renal hemorrhage in a male patient with persistent eosinophilia: highlighting the importance of early diagnosis of eosinophilic granulomatosis with polyangiitis.

Lin J, Wang R, Zhu Y, et al.

Journal of Zhejiang University. Science. B 2025; (26(7)):708-712 doi:10.1631/jzus.B2300940.

Immunological Markers Associated with Skin Manifestations of EGPA.

Brunetto S, Buta F, Gangemi S, Ricciardi L

International journal of molecular sciences 2025; (26(15)) doi:10.3390/ijms26157472.

Initial Hemorrhagic Pericardial Effusion Evolving Into Perimyocarditis: An Atypical Early Presentation of Eosinophilic Granulomatosis With Polyangiitis.

Almatrafi SA, Quqandi SM, Ismail SJ, Alghamdi KA

Cureus 2025; (17(7)):e88155 doi:10.7759/cureus.88155.

The hypereosinophilia dilemma: what's beyond cardiac involvement?

Ivănescu AC, Badea GC, Dan GA

Romanian journal of internal medicine = Revue roumaine de medecine interne 2025; (63(4)):316-322 doi:10.2478/rjim-2025-0018.

Real-world safety and effectiveness of mepolizumab for patients with eosinophilic granulomatosis with polyangiitis in Japan: A subgroup analysis of the MARS study.

Ishii T, Kunishige H, Yoshida M, et al.

Modern rheumatology 2026; (36(2)):272-281 doi:10.1093/mr/roaf096.

Clinical, Biomarker, and Radiological Progression from Asthma to Systemic Eosinophilic Granulomatosis with Polyangiitis: A Retrospective Cohort Study.

Lu C, Ou C, Deng Y, et al.

Journal of asthma and allergy 2025; (18()):1615-1626 doi:10.2147/JAA.S542255.

Improved long-term prognosis of eosinophilic granulomatosis with polyangiitis: retrospective analysis of 87 patients after biologic therapy introduction in Japan.

Yamashita Y, Masumoto N, Takaoka S, et al.

Scientific reports 2026; (16(1)).