Research & Literature

Urticarial vasculitis and urticarial autoinflammatory syndromes.

Marzano AV, Tavecchio S, Venturini M, et al.

Giornale italiano di dermatologia e venereologia : organo ufficiale, Societa italiana di dermatologia e sifilografia 2015; (150(1)):41-50.

[Severe pulmonary involvement in hypocomplementemic urticarial vasculitis (HUV)].

Raoufi M, Laine M, Amrani HN, et al.

The Pan African medical journal 2016; (24()):285 doi:10.11604/pamj.2016.24.285.8168.

[Hypocomplementemic urticarial vasculitis].

Jachiet M, Flageul B, Bouaziz JD, et al.

La Revue de medecine interne 2018; (39(2)):90-98 doi:10.1016/j.revmed.2017.03.005.

Renal manifestations in hypocomplementic urticarial vasculitis syndrome: Is it a distinct pathology?

AlHermi B, Al Mosawi Z, Mohammed D

Saudi journal of kidney diseases and transplantation : an official publication of the Saudi Center for Organ Transplantation, Saudi Arabia 2017; (28(4)):929-933.

Clinical utility of anti-C1q antibody in primary and secondary vasculitic conditions.

Jayakanthan K, Gupta AN, Mathew J, et al.

International journal of health sciences 2017; (11(5)):3-6.

Hypocomplementemic Urticarial Vasculitis Syndrome with Membranous Nephropathy: Case Report.

Jung SW, Choi YY, Choi IS, et al.

Journal of Korean medical science 2017; (32(12)):2064-2068 doi:10.3346/jkms.2017.32.12.2064.

Hypocomplementemic Urticarial Vasculitis Syndrome With Crescentic Glomerulonephritis.

Salim SA, Yousuf T, Patel A, et al.

The American journal of the medical sciences 2018; (355(2)):195-200 doi:10.1016/j.amjms.2017.04.004.

Epidemiology of hypocomplementaemic urticarial vasculitis (anti-C1q vasculitis).

Sjöwall C, Mandl T, Skattum L, et al.

Rheumatology (Oxford, England) 2018; (57(8)):1400-1407 doi:10.1093/rheumatology/key110.

Mimickers of Urticaria: Urticarial Vasculitis and Autoinflammatory Diseases.

Davis MDP, van der Hilst JCH

The journal of allergy and clinical immunology. In practice 2018; (6(4)):1162-1170 doi:10.1016/j.jaip.2018.05.006.

Treatment of urticarial vasculitis: A systematic review.

Kolkhir P, Grakhova M, Bonnekoh H, et al.

The Journal of allergy and clinical immunology 2019; (143(2)):458-466 doi:10.1016/j.jaci.2018.09.007.

An update on the nomenclature for cutaneous vasculitis.

Caproni M, Verdelli A

Current opinion in rheumatology 2019; (31(1)):46-52 doi:10.1097/BOR.0000000000000563.

Analysis of Anti-C1q Autoantibodies by Western Blot.

Verlemyr A, Truedsson L, Skattum L

Methods in molecular biology (Clifton, N.J.) 2019; (1901()):183-189 doi:10.1007/978-1-4939-8949-2_14.

Successful treatment of normocomplementemic urticarial vasculitis with omalizumab: A report of three cases and literature review.

Rattananukrom T, Svetvilas P, Chanprapaph K

Asian Pacific journal of allergy and immunology 2020; (38(4)):286-289 doi:10.12932/AP-050918-0402.

Dermal C4d Deposition and Neutrophil Alignment Along the Dermal-Epidermal Junction as a Diagnostic Adjunct for Hypocomplementemic Urticarial Vasculitis (Anti-C1q Vasculitis) and Underlying Systemic Disease.

Damman J, Mooyaart AL, Seelen MAJ, van Doorn MBA

The American Journal of dermatopathology 2020; (42(6)):399-406 doi:10.1097/DAD.0000000000001501.

Hypocomplementemic urticarial vasculitis syndrome with gastrointestinal vasculitis and crescentic membranoproliferative glomerulonephritis without immune complex deposits.

Ueki K, Tsuchimoto A, Matsukuma Y, et al.

CEN case reports 2020; (9(1)):30-35 doi:10.1007/s13730-019-00421-4.

[Hypocomplementemic urticarial vasculitis syndrome: a rare but not always benign condition].

Sjöwall C, Skattum L, Olsson M, et al.

Lakartidningen 2019; (116()).

Management of urticarial vasculitis: A worldwide physician perspective.

Kolkhir P, Bonnekoh H, Kocatürk E, et al.

The World Allergy Organization journal 2020; (13(3)):100107 doi:10.1016/j.waojou.2020.100107.

Kidney Involvement in Hypocomplementemic Urticarial Vasculitis Syndrome-A Case-Based Review.

Ion O, Obrișcă B, Ismail G, et al.

Journal of clinical medicine 2020; (9(7)) doi:10.3390/jcm9072131.

A case report of hypocomplementemic urticarial vasculitis presenting with membranoproliferative glomerulonephritis.

Vallianou K, Skalioti C, Liapis G, et al.

BMC nephrology 2020; (21(1)):351 doi:10.1186/s12882-020-02001-6.

Diagnosis and management of leukocytoclastic vasculitis.

Fraticelli P, Benfaremo D, Gabrielli A

Internal and emergency medicine 2021; (16(4)):831-841 doi:10.1007/s11739-021-02688-x.

A novel histopathological scoring system to distinguish urticarial vasculitis from chronic spontaneous urticaria.

Puhl V, Bonnekoh H, Scheffel J, et al.

Clinical and translational allergy 2021; (11(2)):e12031 doi:10.1002/clt2.12031.

Hypocomplementemic urticarial vasculitis syndrome presenting with bilateral scleritis.

Berry EC, Wells J, Morey A, Anantharajah A

BMJ case reports 2021; (14(5)) doi:10.1136/bcr-2020-240041.

[Update on etiopathogenesis of small vessel vasculitis].

Arnold S, Holl-Ulrich K, Müller A, et al.

Zeitschrift fur Rheumatologie 2022; (81(4)):270-279 doi:10.1007/s00393-021-01155-4.

Biopsy-proven kidney involvement in hypocomplementemic urticarial vasculitis.

Corthier A, Jachiet M, Bertin D, et al.

BMC nephrology 2022; (23(1)):67 doi:10.1186/s12882-022-02689-8.

Urticarial vasculitis: Clinical and laboratory findings with a particular emphasis on differential diagnosis.

Marzano AV, Maronese CA, Genovese G, et al.

The Journal of allergy and clinical immunology 2022; (149(4)):1137-1149 doi:10.1016/j.jaci.2022.02.007.

Hypocomplementemic Urticarial Vasculitis Syndrome or Systemic Lupus Erythematosus in Evolution?

Kesarwani V, Phachu D, Trivedi R

Cureus 2022; (14(3)):e23429 doi:10.7759/cureus.23429.

DNASE1L3 deficiency, new phenotypes, and evidence for a transient type I IFN signaling.

Tusseau M, Lovšin E, Samaille C, et al.

Journal of clinical immunology 2022; (42(6)):1310-1320 doi:10.1007/s10875-022-01287-5.

Efficacy and safety of omalizumab therapy in urticaria vasculitis.

Petrelli F, Giannini D, Bilia S, et al.

Frontiers in allergy 2022; (3()):952079 doi:10.3389/falgy.2022.952079.

Correct approach in urticarial vasculitis made early diagnosis of lupus nephritis possible: a case report.

Smets K, Van Baelen A, Sprangers B, De Haes P

Journal of medical case reports 2022; (16(1)):314 doi:10.1186/s13256-022-03477-6.

Hypocomplementemic Urticarial Vasculitis Associated With Hashimoto's Thyroiditis and Hepatitis B Virus Infection: A Case Report.

Scurtu LG, Costache M, Opriș-Belinski D, Simionescu O

Cureus 2022; (14(9)):e29643 doi:10.7759/cureus.29643.

[Renal manifestations in vasculitides of small and medium-sized vessels].

Schneider J, Venhoff N

Zeitschrift fur Rheumatologie 2022; (81(10)):851-857 doi:10.1007/s00393-022-01282-6.

Hypocomplementemic Urticarial Vasculitis Syndrome Masquerading as Systemic Lupus Erythematosus: A Case Report.

Mehta JP, Jang CQH, Fahim P, et al.

Glomerular diseases 2022; (2(4)):189-193 doi:10.1159/000525942.

Hypocomplementemic urticarial vasculitis case with hemophagocytic lymphohistiocytosis following SARS-CoV-2 mRNA vaccination.

Iwamura N, Eguchi K, Koga T, et al.

Immunological medicine 2023; (46(2)):97-107 doi:10.1080/25785826.2023.2193286.

Urticarial Vasculitis Differs From Chronic Spontaneous Urticaria in Time to Diagnosis, Clinical Presentation, and Need for Anti-Inflammatory Treatment: An International Prospective UCARE Study.

Bonnekoh H, Jelden-Thurm J, Allenova A, et al.

The journal of allergy and clinical immunology. In practice 2023; (11(9)):2900-2910.e21 doi:10.1016/j.jaip.2023.06.030.

Differential diagnosis between urticarial vasculitis and chronic spontaneous urticaria: An international Delphi survey.

Krause K, Bonnekoh H, Jelden-Thurm J, et al.

Clinical and translational allergy 2023; (13(10)):e12305 doi:10.1002/clt2.12305.

Breaking Out of the Hive: A Case Report on Hypocomplementemic Urticarial Vasculitis Syndrome.

Louis M, Akhtar A, Gibson B

Cureus 2024; (16(5)):e60986 doi:10.7759/cureus.60986.

Case Report: Hypocomplementemic urticarial vasculitis syndrome in a pediatric patient with complement factor 1 deficiency.

Lin S, Kafisheh D, Elder ME

Frontiers in pediatrics 2024; (12()):1448094 doi:10.3389/fped.2024.1448094.

Managing Urticarial Vasculitis: A Clinical Decision-Making Algorithm Based on Expert Consensus.

Rothermel ND, Vera Ayala C, Gonçalo M, et al.

American journal of clinical dermatology 2025; (26(1)):61-75 doi:10.1007/s40257-024-00902-y.

A Case of Hypocomplementemic Urticarial Vasculitis Syndrome With Severe Renal and Gastrointestinal Involvement.

Jost L, Helmchen BM, Osthoff M, Nigg Calanca L

Cureus 2024; (16(10)):e72113 doi:10.7759/cureus.72113.

Urticarial vasculitis.

Ergun T

Current opinion in rheumatology 2025; (37(1)):45-50 doi:10.1097/BOR.0000000000001058.

Off-label use of biologics in urticarial vasculitis: a European retrospective cohort study.

Maisonobe L, Korganow AS, Berti A, et al.

Rheumatology (Oxford, England) 2025; (64(7)):4309-4315 doi:10.1093/rheumatology/keaf039.

Rare presentation of hypocomplementaemic urticarial vasculitis syndrome (HUVS) overlapping with systemic erythematosus lupus (SLE) and small lymphocytic lymphoma (SLL).

Chao C, Aksoy M, Varma N, Tagoe CE

BMJ case reports 2025; (18(2)) doi:10.1136/bcr-2024-262329.

Hypocomplementemic Urticarial Vasculitis Syndrome: A Rare Form of Vasculitis.

Singh SK, Gupta M, Rani S, Singh P

Cureus 2025; (17(1)):e78227 doi:10.7759/cureus.78227.

Current therapeutic options for adult patients with urticarial vasculitis: A scoping review.

Groleau AS, Mereniuk A, Makhzoum JP

Journal of the American Academy of Dermatology 2025; (93(2)):423-428 doi:10.1016/j.jaad.2025.03.056.

Treatment and long-term follow-up of pediatric patients with hypocomplementemic urticarial vasculitis syndrome (HUVS): a case-based review.

Taş Ö, Aydın F, Özçakar ZB

Clinical rheumatology 2025; (44(7)):3109-3118 doi:10.1007/s10067-025-07509-6.

Urticarial hypocomplementemic vasculitis syndrome and systemic lupus erythematosus: a case report and review of the literature.

Ouerdani Y, Ben Achour T, Ben Hmid A, et al.

Frontiers in immunology 2025; (16()):1649699 doi:10.3389/fimmu.2025.1649699.

Respiratory Involvement During the Course of Hypocomplementemic Urticarial Vasculitis: A Case Report.

Dorian L, Peché R, Guiot J, Van Laethem S

Cureus 2025; (17(8)):e89813 doi:10.7759/cureus.89813.

Childhood-onset hypocomplementaemic urticarial vasculitis in France: phenotypic and genotypic diversity in 10 children.

Bianchi C, Melki I, Sisirak V, et al.

Pediatric rheumatology online journal 2026; (24(1)).

Clinical Profile of Patients with Urticarial Vasculitis in China: A Retrospective of 142 Cases.

Hu W, Zhu Y, Geng S, et al.

Journal of inflammation research 2026; (19()):576374 doi:10.2147/JIR.S576374.

Hypocomplementemic urticarial vasculitis: a rare presentation revealing systemic lupus erythematosus and Sjögren's disease.

Taharboucht S, Mehiris C, Bellil S, et al.

Reumatismo 2026; (78(2)) doi:10.4081/reumatismo.2026.1930.

Discordance between disease activity and long-term outcomes in DNASE1L3 deficiency: a multicentre longitudinal cohort study.

Abdwani R, Al Abrawi S, Aljaberi N, et al.

Lupus science & medicine 2026; (13(2)) doi:10.1136/lupus-2026-002175.

Unraveling the Clinical Spectrum of DNASE1L3 Deficiency: Insights from Case Series and Systematic Literature Review.

Ercan Emreol H, Unal D, Sag E, et al.

Current rheumatology reports 2026; (28(1)).