Research & Literature

Treatment of systemic necrotizing vasculitides in patients aged sixty-five years or older: results of a multicenter, open-label, randomized controlled trial of corticosteroid and cyclophosphamide-based induction therapy.

Pagnoux C, Quéméneur T, Ninet J, et al.

Arthritis & rheumatology (Hoboken, N.J.) 2015; (67(4)):1117-27 doi:10.1002/art.39011.

Cutaneous polyarteritis nodosa.

Matteoda MA, Stefano PC, Bocián M, et al.

Anais brasileiros de dermatologia 2015; (90(3 Suppl 1)):188-90.

Single organ variant of polyarteritis nodosa in epididymis.

Garg K, Dawson L

Journal of cancer research and therapeutics 2015; (11(3)):662 doi:10.4103/0973-1482.138133.

Glucocorticoid-induced Osteoporosis.

Whittier X, Saag KG

Rheumatic diseases clinics of North America 2016; (42(1)):177-89, x.

Predictive factors for mortality in elderly Japanese patients with severe microscopic polyangiitis: A retrospective single-center study.

Abe Y, Tamura N, Yang KS, et al.

Modern rheumatology 2017; (27(2)):315-319 doi:10.1080/14397595.2016.1205778.

[Beware, polyarteritis nodosa still exists in nephrology!]

Perrin J, Carvelli J, Gondouin B, et al.

Nephrologie & therapeutique 2016; (12(6)):463-467 doi:10.1016/j.nephro.2016.03.007.

Wunderlich's syndrome as a manifestation of polyarteritis nodosa.

Beirão P, Teixeira L, Pereira P, Coelho ML

BMJ case reports 2017; (2017()) doi:10.1136/bcr-2016-218478.

Successful surgical intervention for rectal perforation due to polyarteritis nodosa: report of a case.

Yoshiya K, Imamura Y, Nakaji Y, et al.

Surgical case reports 2017; (3(1)):43 doi:10.1186/s40792-017-0316-0.

Birmingham vasculitis activity score at diagnosis is a significant predictor of relapse of polyarteritis nodosa.

Oh YJ, Ahn SS, Park ES, et al.

Rheumatology international 2017; (37(5)):685-694 doi:10.1007/s00296-017-3706-5.

Are the 1990 American College of Rheumatology vasculitis classification criteria still valid?

Seeliger B, Sznajd J, Robson JC, et al.

Rheumatology (Oxford, England) 2017; (56(7)):1154-1161 doi:10.1093/rheumatology/kex075.

Cutaneous Manifestations of Medium- and Large-Vessel Vasculitis.

Chasset F, Francès C

Clinical reviews in allergy & immunology 2017; (53(3)):452-468 doi:10.1007/s12016-017-8612-9.

Mononeuritis multiplex in a patient with cutaneous arteritis diagnosed by skin biopsy.

Isahaya K, Shiraishi M, Tanaka K, et al.

Rinsho shinkeigaku = Clinical neurology 2017; (57(6)):307-310 doi:10.5692/clinicalneurol.cn-001013.

Comparing polyarteritis nodosa in children and adults: a single center study.

Erden A, Batu ED, Sönmez HE, et al.

International journal of rheumatic diseases 2017; (20(8)):1016-1022 doi:10.1111/1756-185X.13120.

Refractory cutaneous polyarteritis nodosa: Successful treatment with etanercept.

Inoue N, Shimizu M, Mizuta M, et al.

Pediatrics international : official journal of the Japan Pediatric Society 2017; (59(6)):751-752 doi:10.1111/ped.13283.

Association of five-factor score with the mortality in Japanese patients with polyarteritis nodosa.

Abe Y, Tada K, Yamaji K, et al.

Modern rheumatology 2018; (28(2)):308-312 doi:10.1080/14397595.2017.1337265.

Treatment of membranous nephropathy: time for a paradigm shift.

Ruggenenti P, Fervenza FC, Remuzzi G

Nature reviews. Nephrology 2017; (13(9)):563-579 doi:10.1038/nrneph.2017.92.

Cutaneous polyarteritis nodosa causing refractory skin deformation and pigmentation as sequel.

Okada K, Nakamori R, Mizutani H, Yamanaka K

Anais brasileiros de dermatologia 2017; (92(5 Suppl 1)):53-55 doi:10.1590/abd1806-4841.20175696.

[The changing face of medium-sized vasculitis].

Parada-Turska J, Turska M

Wiadomosci lekarskie (Warsaw, Poland : 1960) 2018; (71(1 pt 1)):64-72.

Case Report: Polyarteritis nodosa or complicated Henoch-Schonlein purpura (IgAV), a rare case.

Hasanzadeh S, Alavi SM, Masnavi E, et al.

F1000Research 2018; (7()):49 doi:10.12688/f1000research.13295.2.

An update on the nomenclature for cutaneous vasculitis.

Caproni M, Verdelli A

Current opinion in rheumatology 2019; (31(1)):46-52 doi:10.1097/BOR.0000000000000563.

Eosinophilic Granulomatosis with Polyangiitis (Churg-Strauss).

Nguyen Y, Guillevin L

Seminars in respiratory and critical care medicine 2018; (39(4)):471-481 doi:10.1055/s-0038-1669454.

Polyarteritis Nodosa Neurologic Manifestations.

de Boysson H, Guillevin L

Neurologic clinics 2019; (37(2)):345-357 doi:10.1016/j.ncl.2019.01.007.

Glucocorticoid-induced osteoporosis update.

Adami G, Saag KG

Current opinion in rheumatology 2019; (31(4)):388-393 doi:10.1097/BOR.0000000000000608.

[Cutaneous alterations in vasculitides : Part 2: Special aspects of diseases of large, medium and small vessels].

Sunderkötter C, Michl C

Der Internist 2019; (60(8)):805-813 doi:10.1007/s00108-019-0642-3.

Lupus nephritis complicated by cytomegalovirus colitis, aspergillosis and brain abscess.

Campos Costa F, Freitas J, Oliveira M, Malcata A

Lupus 2019; (28(12)):1495-1497 doi:10.1177/0961203319872549.

Management of glucocorticoid-related osteoporotic vertebral fracture.

Wong SPY, Mok CC

Osteoporosis and sarcopenia 2020; (6(1)):1-7 doi:10.1016/j.afos.2020.02.002.

Polyarteritis nodosa and deficiency of adenosine deaminase 2 - Shared genealogy, generations apart.

Huang Z, Li T, Nigrovic PA, Lee PY

Clinical immunology (Orlando, Fla.) 2020; (215()):108411 doi:10.1016/j.clim.2020.108411.

Improving quality of life in vasculitis patients.

Aitken M, Basu N

Rheumatology (Oxford, England) 2020; (59(Suppl 3)):iii132-iii135 doi:10.1093/rheumatology/kez546.

Putting the Pieces Into Place: A Case of Systemic Polyarteritis Nodosa.

Brodell D, Scott G, Plovanich M

Cureus 2020; (12(6)):e8442 doi:10.7759/cureus.8442.

Fluctuating facial edema as a rare manifestation of cutaneous polyarteritis nodosa: Case report and review of the literature.

Gaviria A, Patino W, Ruiz M, et al.

Journal of cutaneous pathology 2020; (47(11)):1076-1079 doi:10.1111/cup.13833.

Manifestations, clinical course and prognostic markers in cutaneous polyarteritis nodosa.

Munera-Campos M, Bielsa I, Martínez-Morillo M, et al.

Journal der Deutschen Dermatologischen Gesellschaft = Journal of the German Society of Dermatology : JDDG 2020; (18(11)):1250-1259 doi:10.1111/ddg.14271.

Anti-tumour necrosis factor treatment for the prevention of ischaemic events in patients with deficiency of adenosine deaminase 2 (DADA2).

Cooray S, Omyinmi E, Hong Y, et al.

Rheumatology (Oxford, England) 2021; (60(9)):4373-4378 doi:10.1093/rheumatology/keaa837.

Polyarteritis Nodosa: A Systematic Review of Test Accuracy and Benefits and Harms of Common Treatments.

Lin YC, Kalot MA, Husainat NM, et al.

ACR open rheumatology 2021; (3(2)):91-100 doi:10.1002/acr2.11189.

Clinical Approach to Diagnosis and Therapy of Polyarteritis Nodosa.

Hočevar A, Tomšič M, Perdan Pirkmajer K

Current rheumatology reports 2021; (23(3)):14 doi:10.1007/s11926-021-00983-2.

[Use of new diagnostic criteria for reclassification of polyarteritis nodosa].

Huang Q, Zhao L, Zhou JX, et al.

Zhonghua nei ke za zhi 2021; (60(3)):239-242 doi:10.3760/cma.j.cn112138-20200619-00603.

Expanding spectrum of DADA2: a review of phenotypes, genetics, pathogenesis and treatment.

Pinto B, Deo P, Sharma S, et al.

Clinical rheumatology 2021; (40(10)):3883-3896 doi:10.1007/s10067-021-05711-w.

2021 American College of Rheumatology/Vasculitis Foundation Guideline for the Management of Polyarteritis Nodosa.

Chung SA, Gorelik M, Langford CA, et al.

Arthritis & rheumatology (Hoboken, N.J.) 2021; (73(8)):1384-1393 doi:10.1002/art.41776.

2021 American College of Rheumatology/Vasculitis Foundation Guideline for the Management of Polyarteritis Nodosa.

Chung SA, Gorelik M, Langford CA, et al.

Arthritis care & research 2021; (73(8)):1061-1070 doi:10.1002/acr.24633.

Fluorodeoxyglucose positron emission tomography-computed tomography findings in a first series of 10 patients with polyarteritis nodosa.

Fagart A, Machet T, Collet G, et al.

Rheumatology (Oxford, England) 2022; (61(4)):1663-1668 doi:10.1093/rheumatology/keab591.

TNF inhibition in vasculitis management in adenosine deaminase 2 deficiency (DADA2).

Deuitch NT, Yang D, Lee PY, et al.

The Journal of allergy and clinical immunology 2022; (149(5)):1812-1816.e6 doi:10.1016/j.jaci.2021.10.030.

A Rare Presentation of Polyarteritis Nodosa.

Robinson C, Yasin Z, Patel P, Zebda H

Cureus 2022; (14(2)):e21925 doi:10.7759/cureus.21925.

[Recommendations of diagnosis and treatment of polyarteritis nodosa].

Mansur M, Da ZY, Guo JT, et al.

Zhonghua nei ke za zhi 2022; (61(7)):749-755 doi:10.3760/cma.j.cn112138-20211201-00852.

Case report: Polyarteritis nodosa as a substrate for a massive myocardial infarction.

Solis-Jimenez F, Gonzalez-Ortiz A, Larios-Lara JH, et al.

Frontiers in cardiovascular medicine 2022; (9()):1070378 doi:10.3389/fcvm.2022.1070378.

Polyarteritis Nodosa Following mRNA-1273 COVID-19 Vaccination: Case Study and Review of Immunological Mechanisms.

Srichawla BS

Cureus 2023; (15(1)):e33620 doi:10.7759/cureus.33620.

Deficiency of adenosine deaminase 2 (DADA2): Review.

Sharma V, Deo P, Sharma A

Best practice & research. Clinical rheumatology 2023; (37(1)):101844 doi:10.1016/j.berh.2023.101844.

The "Viral" Form of Polyarteritis Nodosa (PAN)-A Distinct Entity: A Case Based Review.

Pașa V, Popa E, Poroch M, et al.

Medicina (Kaunas, Lithuania) 2023; (59(6)) doi:10.3390/medicina59061162.

Clinical features and long-term outcomes of patients with systemic polyarteritis nodosa diagnosed since 2005: Data from 196 patients.

Rohmer J, Nguyen Y, Trefond L, et al.

Journal of autoimmunity 2023; (139()):103093 doi:10.1016/j.jaut.2023.103093.

Ruptured Saccular Aneurysm Caused by Necrotizing Arteritis of the Polyarteritis Nodosa Type in Primary Angiitis of Central Nervous System.

Matsumoto T, Ogura K, Tokugawa J, et al.

International journal of surgical pathology 2024; (32(7)):1364-1367 doi:10.1177/10668969241228292.

Nationwide epidemiological survey of polyarteritis nodosa in Japan in 2020.

Kawazoe M, Nanki T, Saeki K, et al.

Modern rheumatology 2024; (34(6)):1284-1287 doi:10.1093/mr/roae010.

Wunderlich syndrome as a rare complication of polyarteritis nodosa: a case report.

Oliveira D, Martins A, Martins F, et al.

Reumatismo 2024; (76(1)) doi:10.4081/reumatismo.2024.1669.

Central retinal artery occlusion in a child with ADA2 deficiency: a case report.

Sharabati I, Ayesh BM, Qafesha RM, et al.

Annals of medicine and surgery (2012) 2024; (86(4)):2343-2347 doi:10.1097/MS9.0000000000001857.

Early skeletal muscle manifestations in polyarteritis nodosa and ANCA-associated vasculitis.

Shimojima Y, Nomura S, Ushiyama S, et al.

Autoimmunity reviews 2024; (23(7-8)):103602 doi:10.1016/j.autrev.2024.103602.

Polyarteritis nodosa complicated by renal aneurysm and intestinal perforation: A case report.

Ma Y, Luan L, Zhang J, et al.

Medicine 2024; (103(34)):e39445 doi:10.1097/MD.0000000000039445.

Critical Limb Threatening Ischemia Due to Severe Polyarteritis Nodosa.

Yagi I, Yagi S, Nakanishi K, et al.

Internal medicine (Tokyo, Japan) 2025; (64(9)):1355-1358 doi:10.2169/internalmedicine.4149-24.

Page kidney in a case of polyarteritis nodosa.

Demirci Yıldırım T

Forensic science, medicine, and pathology 2025; (21(1)):507-508 doi:10.1007/s12024-024-00904-6.

Polyarteritis nodosa presenting with severe upper gastrointestinal bleeding: a case report.

Xiao XY, Niu Y, Liu PP, et al.

Journal of medical case reports 2024; (18(1)):616 doi:10.1186/s13256-024-04892-7.

The clinical characteristics and treatment outcomes of patients with systemic polyarteritis nodosa: a single-centre study from India.

Jha A, R C, Yadav B, et al.

Rheumatology (Oxford, England) 2025; (64(6)):3710-3717 doi:10.1093/rheumatology/keaf014.

Recommendations for the diagnosis and treatment of anti-neutrophil cytoplasmic autoantibody associated vasculitis.

Morales E, Rúa-Figueroa I, Callejas Rubio JL, et al.

Nefrologia 2025; (45(1)):15-58 doi:10.1016/j.nefroe.2025.01.001.

Sequential central retinal artery occlusion in two brothers: a fight to prevent blindness.

Oliver-Gutierrez D, Subirà O, Zabalza A, et al.

Documenta ophthalmologica. Advances in ophthalmology 2025; (150(2)):105-110 doi:10.1007/s10633-025-10006-5.

Idiopathic polyarteritis nodosa - does it still exist? Viewpoint 1: as our knowledge makes progress, idiopathic polyarteritis nodosa is fading away.

Watts RA

Rheumatology (Oxford, England) 2025; (64(Supplement_1)):i79-i81 doi:10.1093/rheumatology/keae649.

Artificial intelligence challenge of discriminating cutaneous arteritis and polyarteritis nodosa based on hematoxylin-and-eosin images of skin biopsy specimens.

Kashiwa W, Hirata K, Endo H, et al.

Pathology, research and practice 2025; (269()):155915 doi:10.1016/j.prp.2025.155915.

Complex presentation of polyarteritis nodosa: Renal pseudoaneurysm rupture and bowel ischemia: A case report.

Rabaya AF, Ibraheem K, Shawer O, et al.

International journal of surgery case reports 2025; (129()):111172 doi:10.1016/j.ijscr.2025.111172.

Spontaneous accessory renal artery aneurysm rupture as a first presentation of polyarteritis nodosa: a case report and review of literature.

Amro RN, Maraqa L, Abo Jheasha AA, et al.

Annals of medicine and surgery (2012) 2025; (87(6)):3956-3962 doi:10.1097/MS9.0000000000003331.

An 80-year-old female with multiple mononeuropathy: neuroleukemiosis a rare complication of chronic lymphocytic leukaemia.

Morgan C, Srinivasan V, Pohl U, Wakerley BR

Oxford medical case reports 2025; (2025(8)):omaf131 doi:10.1093/omcr/omaf131.

Pediatric-Onset Polyarteritis Nodosa and Deficiency of Adenosine Deaminase 2: Clinical Overlap and Divergence.

Atamyildiz Uçar S, Tunce E, Türkmen Ş, et al.

Journal of clinical rheumatology : practical reports on rheumatic & musculoskeletal diseases 2025; (31(8)):299-305 doi:10.1097/RHU.0000000000002270.

Successful Treatment of Polyarteritis Nodosa With Multifocal Intracranial and Mesenteric Stenoses Using Endovascular Stenting and Tocilizumab.

Nobre M, Carrilho M, Dias A, et al.

Cureus 2025; (17(8)):e89607 doi:10.7759/cureus.89607.

[Polyarteritis nodosa].

Ghrenassia É, Guedon A, Hadjadj J, et al.

La Revue du praticien 2025; (75(5)):541-547.

A Case of Challenging Polyarteritis Nodosa With Critical Limb Ischemia.

Renken L, Zollinger-Read C, Coote A

Cureus 2025; (17(11)):e97257 doi:10.7759/cureus.97257.

Recent pathogenetic insights and therapeutic advances in ANCA-associated vasculitis.

Sagy I, Jayne DRW

Annals of the rheumatic diseases 2026; (85(4)):588-602 doi:10.1016/j.ard.2025.11.024.

Hepatic Manifestations and Response to Treatment in Deficiency of Adenosine Deaminase 2.

Shaik MR, Alao H, Shaik NA, et al.

Liver international : official journal of the International Association for the Study of the Liver 2026; (46(6)):e70660 doi:10.1111/liv.70660.

Temporal artery biopsy in polyarteritis nodosa: a case-based narrative literature review.

Fujikake T, Anegawa M, Wada S, et al.

Clinical rheumatology 2026; (45(7)):4675-4685 doi:10.1007/s10067-026-08183-y.

Asymmetrical muscular disorder with normal creatine kinase (CK) and electromyography (EMG): the challenging diagnosis of muscular polyarteritis nodosa (MPAN), case report and literature review.

Dib A, Lequain H, Fenouil T, et al.

Neurological sciences : official journal of the Italian Neurological Society and of the Italian Society of Clinical Neurophysiology 2026; (47(7)).