Research & Literature

Strokes in Sneddon syndrome without antiphospholipid antibodies.

Bottin L, Francès C, de Zuttere D, et al.

Annals of neurology 2015; (77(5)):817-29 doi:10.1002/ana.24382.

Livedo reticularis: A review of the literature.

Sajjan VV, Lunge S, Swamy MB, Pandit AM

Indian dermatology online journal 2015; (6(5)):315-21 doi:10.4103/2229-5178.164493.

Low dose aspirin and pregnancy: how important is aspirin resistance?

Navaratnam K, Alfirevic A, Alfirevic Z

BJOG : an international journal of obstetrics and gynaecology 2016; (123(9)):1481-7 doi:10.1111/1471-0528.13914.

Deficiency of Adenosine Deaminase Type 2: A Description of Phenotype and Genotype in Fifteen Cases.

Nanthapisal S, Murphy C, Omoyinmi E, et al.

Arthritis & rheumatology (Hoboken, N.J.) 2016; (68(9)):2314-22 doi:10.1002/art.39699.

Recognition of Stroke by EMS is Associated with Improvement in Emergency Department Quality Measures.

Abboud ME, Band R, Jia J, et al.

Prehospital emergency care 2016; (20(6)):729-736 doi:10.1080/10903127.2016.1182602.

Idiopathic livedo racemosa presenting with splenomegaly and diffuse lymphadenopathy.

Bukavina L, Weaver J, Nagy T, et al.

Cutis 2016; (98(4)):E26-E29.

Recent advances in the management of transient ischemic attacks.

Gomez CR, Schneck MJ, Biller J

F1000Research 2017; (6()):1893 doi:10.12688/f1000research.12358.1.

The cutaneous manifestations are significantly related to cerebrovascular in a Serbian cohort of patients with Hughes syndrome.

Stojanovich L, Djokovic A, Stanisavljevic N, Zdravkovic M

Lupus 2018; (27(5)):858-863 doi:10.1177/0961203317751065.

Thrombosis and Anti-phospholipid Syndrome: a 5-Year Update on Treatment.

Chighizola CB, Meroni PL

Current rheumatology reports 2018; (20(7)):44 doi:10.1007/s11926-018-0741-5.

Cognitive and psychiatric changes as first clinical presentation in Sneddon syndrome.

Fabiani G, Martins R, Koppe GL, et al.

Dementia & neuropsychologia 2018; (12(2)):216-219 doi:10.1590/1980-57642018dn12-020016.

Vasculopathy, Immunodeficiency, and Bone Marrow Failure: The Intriguing Syndrome Caused by Deficiency of Adenosine Deaminase 2.

Lee PY

Frontiers in pediatrics 2018; (6()):282 doi:10.3389/fped.2018.00282.

EULAR recommendations for the management of antiphospholipid syndrome in adults.

Tektonidou MG, Andreoli L, Limper M, et al.

Annals of the rheumatic diseases 2019; (78(10)):1296-1304 doi:10.1136/annrheumdis-2019-215213.

Sneddon Syndrome: A Comprehensive Overview.

Samanta D, Cobb S, Arya K

Journal of stroke and cerebrovascular diseases : the official journal of National Stroke Association 2019; (28(8)):2098-2108 doi:10.1016/j.jstrokecerebrovasdis.2019.05.013.

[Cutaneous alterations in vasculitides : Part 2: Special aspects of diseases of large, medium and small vessels].

Sunderkötter C, Michl C

Der Internist 2019; (60(8)):805-813 doi:10.1007/s00108-019-0642-3.

Effect of Standard vs Intensive Blood Pressure Control on the Risk of Recurrent Stroke: A Randomized Clinical Trial and Meta-analysis.

Kitagawa K, Yamamoto Y, Arima H, et al.

JAMA neurology 2019; (76(11)):1309-1318 doi:10.1001/jamaneurol.2019.2167.

Rivaroxaban Versus Vitamin K Antagonist in Antiphospholipid Syndrome: A Randomized Noninferiority Trial.

Ordi-Ros J, Sáez-Comet L, Pérez-Conesa M, et al.

Annals of internal medicine 2019; (171(10)):685-694 doi:10.7326/M19-0291.

Mechanisms of kidney disease in Sneddon's syndrome: Case report and literature review
.

Ghislain L, Aydin S, Marot L, et al.

Clinical nephrology 2020; (93(4)):209-214 doi:10.5414/CN109748.

Livedo Racemosa: Clinical, Laboratory, and Histopathological Findings in 33 Patients.

Pincelli MS, Echavarria AMJ, Criado PR, et al.

The international journal of lower extremity wounds 2021; (20(1)):22-28 doi:10.1177/1534734619896938.

Lipid-lowering treatment in secondary prevention of ischaemic cerebrovascular disease.

Climent E, Benaiges D, Pedro-Botet J

Clinica e investigacion en arteriosclerosis : publicacion oficial de la Sociedad Espanola de Arteriosclerosis 2020; (32(4)):175-182 doi:10.1016/j.arteri.2019.12.002.

BE-FAST: A Sensitive Screening Tool to Identify In-Hospital Acute Ischemic Stroke.

El Ammar F, Ardelt A, Del Brutto VJ, et al.

Journal of stroke and cerebrovascular diseases : the official journal of National Stroke Association 2020; (29(7)):104821 doi:10.1016/j.jstrokecerebrovasdis.2020.104821.

Livedo racemosa in neurological diseases: an update on the differential diagnoses.

Mitri F, Enk A, Bersano A, Kraemer M

European journal of neurology 2020; (27(10)):1832-1843 doi:10.1111/ene.14390.

Livedo Racemosa - The Pathophysiology of Decompression-Associated Cutis Marmorata and Right/Left Shunt.

Hartig F, Reider N, Sojer M, et al.

Frontiers in physiology 2020; (11()):994 doi:10.3389/fphys.2020.00994.

Superficial Siderosis and Microbleed Restricted in Cortex Might Be Correlated to Atrophy and Cognitive Decline in Sneddon's Syndrome.

Yao M, Zhao J, Jiang N, et al.

Frontiers in neurology 2020; (11()):1035 doi:10.3389/fneur.2020.01035.

Characteristic imaging features of neurovascular involvement in primary Sneddon's syndrome: an analysis of 12 cases.

Yilmaz E, Arsava EM, Gocmen R, et al.

Neurological sciences : official journal of the Italian Neurological Society and of the Italian Society of Clinical Neurophysiology 2021; (42(6)):2363-2369 doi:10.1007/s10072-020-04621-0.

Three cases of Sneddon syndrome: A comparison with lymphocytic thrombophilic arteritis.

Ting S, Kelly RI

The Australasian journal of dermatology 2021; (62(2)):e272-e275 doi:10.1111/ajd.13523.

Sneddon syndrome: a comprehensive clinical review of 53 patients.

Starmans NLP, van Dijk MR, Kappelle LJ, Frijns CJM

Journal of neurology 2021; (268(7)):2450-2457 doi:10.1007/s00415-021-10407-x.

Freiberg's Infarction as the First Clinical Presentation of Sneddon Syndrome.

Samanta D, Cobb S

Journal of pediatric neurosciences 2020; (15(3)):290-293 doi:10.4103/jpn.JPN_159_19.

Age-Dependent Differences in the Rate and Symptoms of TIA Mimics in Patients Presenting With a Suspected TIA to a Neurological Emergency Room.

Ippen FM, Walter F, Hametner C, et al.

Frontiers in neurology 2021; (12()):644223 doi:10.3389/fneur.2021.644223.

Primary central nervous system vasculitis - An update on diagnosis, differential diagnosis and treatment.

Kraemer M, Berlit P

Journal of the neurological sciences 2021; (424()):117422 doi:10.1016/j.jns.2021.117422.

Concomitant myocardial injury and valvular disease in Sneddon syndrome: a case report.

Scadi S, Huttin O, Selton Suty C, Wahl D

European heart journal. Case reports 2021; (5(6)):ytab211 doi:10.1093/ehjcr/ytab211.

The diagnostic value of skin biopsies in Sneddon syndrome.

Starmans NLP, Zoetemeyer S, van Dijk MR, et al.

PloS one 2021; (16(6)):e0253365 doi:10.1371/journal.pone.0253365.

Vasculitic peripheral neuropathy in deficiency of adenosine deaminase 2.

Carneiro DR, Rebelo O, Matos A, et al.

Neuromuscular disorders : NMD 2021; (31(9)):891-895 doi:10.1016/j.nmd.2021.05.001.

Initial Progressions of Carotid Artery Plaque Are Associated with Risk Factors of Cardiovascular Disease.

Ishikawa M, Nagai M, Matsumoto E, Hashimoto M

Journal of medical ultrasound 2021; (29(3)):187-194 doi:10.4103/JMU.JMU_107_20.

Antiphospholipid-negative Sneddon's syndrome: A comprehensive overview of a rare entity.

Assan F, Bottin L, Francès C, et al.

Annales de dermatologie et de venereologie 2022; (149(1)):3-13 doi:10.1016/j.annder.2021.08.007.

Maternal Stroke Associated With Pregnancy.

Miller EC

Continuum (Minneapolis, Minn.) 2022; (28(1)):93-121 doi:10.1212/CON.0000000000001078.

More Than Just the Target: Blood Pressure, Stroke, and Vascular Cognitive Impairment.

Sandset EC

Stroke 2022; (53(4)):1052-1053 doi:10.1161/STROKEAHA.122.038387.

Emergency Medical Services Prenotification is Associated with Reduced Odds of In-Hospital Mortality in Stroke Patients.

Nielsen VM, Song G, DeJoie-Stanton C, Zachrison KS

Prehospital emergency care 2023; (27(5)):639-645 doi:10.1080/10903127.2022.2079784.

Recent advances in the management of transient ischemic attacks.

Ortiz-Garcia J, Gomez CR, Schneck MJ, Biller J

Faculty reviews 2022; (11()):19 doi:10.12703/r/11-19.

Comprehensive Assessment of Acute Isolated or Prominent Dysarthria in the Emergency Department: A Neuro-Emergency Expert's Experience beyond Stroke.

Lee SH, Ha SO, Kim JH, et al.

Brain sciences 2022; (12(8)) doi:10.3390/brainsci12081047.

Triple positive profile in antiphospholipid syndrome: prognosis, relapse and management from a retrospective multicentre study.

Laurent C, Ricard L, Nguyen Y, et al.

RMD open 2023; (9(1)) doi:10.1136/rmdopen-2022-002534.

The CADA-MRIT: An MRI Inventory Tool for Evaluating Cerebral Lesions in CADASIL Across Cohorts.

Zhang R, Chen CH, Tezenas Du Montcel S, et al.

Neurology 2023; (101(17)):e1665-e1677 doi:10.1212/WNL.0000000000207713.

Cognitive and psychiatric signs revealing Sneddon syndrome: A case report.

Karoui M, Baklouti E, Ben Mohamed D, et al.

Clinical case reports 2023; (11(10)):e8013 doi:10.1002/ccr3.8013.

Current perspectives on prevention of vascular cognitive impairment and promotion of vascular brain health.

Kalaria RN, Akinyemi RO, Paddick SM, Ihara M

Expert review of neurotherapeutics 2024; (24(1)):25-44 doi:10.1080/14737175.2023.2273393.

Sneddon's Syndrome and the Capability to Work: With Regard to a Clinical Case.

Ribeiro R, Saldanha N, Matos P, et al.

Indian journal of occupational and environmental medicine 2024; (28(1)):83-85 doi:10.4103/ijoem.ijoem_247_23.

Monogenic causes of cerebral small vessel disease and stroke.

Guey S, Chabriat H

Handbook of clinical neurology 2024; (204()):273-287 doi:10.1016/B978-0-323-99209-1.00018-1.

Comprehensive insights of Sneddon syndrome: A clinical perspective.

Alazzam AY

Journal of central nervous system disease 2024; (16()):11795735241308767 doi:10.1177/11795735241308767.

Associations Between Prenotification and Time to Management in Acute Stroke Patients Transported by Emergency Medical Services.

Jeong YJ, Kim KH, Park JH, et al.

The Journal of emergency medicine 2025; (74()):77-85 doi:10.1016/j.jemermed.2025.02.005.

Emergency MRI as the First Imaging Modality in Acute Stroke: Effect on Diagnostic Performance and Outcomes.

Wang Z, Liu X, Xia Y, et al.

Cerebrovascular diseases (Basel, Switzerland) 2026; (55(2)):201-210 doi:10.1159/000547095.

Pediatric Sneddon syndrome presenting with early-onset liver fibrosis: a rare case report.

Awad QN, Makhlouf TZ, Zhour MF, et al.

Oxford medical case reports 2025; (2025(8)):omaf153 doi:10.1093/omcr/omaf153.

Development of 2023 ACR/EULAR Antiphospholipid Syndrome Classification Criteria, Phase III-A/B Report: Defining and Structuring the Clinical and Laboratory Domains.

Barbhaiya M, Zuily S, Amigo MC, et al.

Current rheumatology reports 2025; (27(1)):41 doi:10.1007/s11926-025-01202-y.

Maternal mortality related to cerebrovascular disease in Turkey (2012-2019): a national registry-based analysis.

Koksal Z, Sahlar TE, Baydilli MB, Yucel A

European journal of obstetrics, gynecology, and reproductive biology 2026; (321()):115063 doi:10.1016/j.ejogrb.2026.115063.

Long-term clinical progression of Sneddon syndrome associated with antiphospholipid syndrome.

Paes BP, da Silva JCRB, de Carvalho PM, Ferreira AGF

Dementia & neuropsychologia 2026; (20()):e2025450 doi:10.1590/1980-5764-DN-2025-0450.

ALIGNED Network for rare cerebrovascular diseases: methodology and preliminary results.

De Toma C, Potenza A, Rifino N, et al.

Neurological sciences : official journal of the Italian Neurological Society and of the Italian Society of Clinical Neurophysiology 2026; (47(7)).

Clinicopathological features of lymphocytic thrombophilic arteritis and the relationship with livedoid vasculopathy - a case series of 36 patients.

Gan C, Wee E, Johnson D, Kelly R

The British journal of dermatology 2026; doi:10.1093/bjd/ljag273.