Research & Literature

Myocardial Ischemia Secondary to Synthetic Cannabinoid (K2) Use in Pediatric Patients.

Clark BC, Georgekutty J, Berul CI

The Journal of pediatrics 2015; (167(3)):757-61.e1.

Long-Term Prostaglandin E1 Infusion for Newborns with Critical Congenital Heart Disease.

Aykanat A, Yavuz T, Özalkaya E, et al.

Pediatric cardiology 2016; (37(1)):131-4 doi:10.1007/s00246-015-1251-0.

The Relentless Effects of the Fontan Paradox.

Rychik J

Seminars in thoracic and cardiovascular surgery. Pediatric cardiac surgery annual 2016; (19(1)):37-43.

Outcomes of multistage palliation of infants with functional single ventricle and heterotaxy syndrome.

Alsoufi B, McCracken C, Schlosser B, et al.

The Journal of thoracic and cardiovascular surgery 2016; (151(5)):1369-77.e2.

Coil occlusion of aberrant arteries to pulmonary sequestration in a case with pulmonary atresia with intact ventricular septum: successful treatment of repetitive myocardial ischaemic attacks.

Ono A, Hayabuchi Y, Kagami S

Cardiology in the young 2017; (27(1)):193-195 doi:10.1017/S1047951116001037.

Outcomes After Decompression of the Right Ventricle in Infants With Pulmonary Atresia With Intact Ventricular Septum Are Associated With Degree of Tricuspid Regurgitation: Results From the Congenital Catheterization Research Collaborative.

Petit CJ, Glatz AC, Qureshi AM, et al.

Circulation. Cardiovascular interventions 2017; (10(5)) doi:10.1161/CIRCINTERVENTIONS.116.004428.

Imaging adult patients with Fontan circulation.

Ginde S, Goot BH, Frommelt PC

Current opinion in cardiology 2017; (32(5)):521-528 doi:10.1097/HCO.0000000000000422.

Prenatal Echocardiographic Predictors of Postnatal Management Strategy in the Fetus with Right Ventricle Hypoplasia and Pulmonary Atresia or Stenosis.

Cao L, Tian Z, Rychik J

Pediatric cardiology 2017; (38(8)):1562-1568 doi:10.1007/s00246-017-1696-4.

Dor procedure for pulmonary atresia with intact ventricular septum in an infant.

Kang Y, Kwak JG, Kim ER, Kim WH

Interactive cardiovascular and thoracic surgery 2018; (26(2)):348-349 doi:10.1093/icvts/ivx285.

"There's no acknowledgement of what this does to people": A qualitative exploration of mental health among parents of children with critical congenital heart defects.

Woolf-King SE, Arnold E, Weiss S, Teitel D

Journal of clinical nursing 2018; (27(13-14)):2785-2794 doi:10.1111/jocn.14275.

The Fontan Procedure for Single-Ventricle Physiology.

Jones MB

Critical care nurse 2018; (38(1)):e1-e10 doi:10.4037/ccn2018994.

Is one-and-a-half better than two?

Barron DJ

Translational pediatrics 2018; (7(1)):9-10 doi:10.21037/tp.2017.08.04.

Long-term outcomes of single-ventricle palliation for pulmonary atresia with intact ventricular septum: Fontan survivors remain at risk of late myocardial ischaemia and death.

Elias P, Poh CL, du Plessis K, et al.

European journal of cardio-thoracic surgery : official journal of the European Association for Cardio-thoracic Surgery 2018; (53(6)):1230-1236 doi:10.1093/ejcts/ezy038.

Transthoracic Echocardiographic Assessment of Coronary Flow in the Diagnosis of Right Ventricular-Dependent Coronary Circulation in Pulmonary Atresia with Intact Ventricular Septum.

Peterson RE, Freire G, Marino CJ, Jureidini SB

Pediatric cardiology 2018; (39(5)):967-975 doi:10.1007/s00246-018-1846-3.

Pulmonary atresia with intact ventricular septum and congenital left ventricular aneurysm.

Ng B, Hickok R, Stapleton G, Karl T

Cardiology in the young 2018; (28(6)):876-878 doi:10.1017/S1047951117002992.

Echocardiographic parameters associated with biventricular circulation and right ventricular growth following right ventricular decompression in patients with pulmonary atresia and intact ventricular septum: Results from a multicenter study.

Maskatia SA, Petit CJ, Travers CD, et al.

Congenital heart disease 2018; (13(6)):892-902 doi:10.1111/chd.12671.

Long-term outcomes after intervention for pulmonary atresia with intact ventricular septum.

Wright LK, Knight JH, Thomas AS, et al.

Heart (British Cardiac Society) 2019; (105(13)):1007-1013 doi:10.1136/heartjnl-2018-314124.

Stenting of the ductus arteriosus for ductal-dependent pulmonary blood flow-current techniques and procedural considerations.

Aggarwal V, Petit CJ, Glatz AC, et al.

Congenital heart disease 2019; (14(1)):110-115 doi:10.1111/chd.12709.

[Percutaneous management of pulmonary atresia with intact ventricular septum and critical pulmonary stenosis].

Vall Camell M, Rodríguez-Fanjul J, Bautista Rodríguez C, et al.

Anales de pediatria 2019; (91(5)):336-343 doi:10.1016/j.anpedi.2018.10.020.

Pulmonary Atresia With Intact Ventricular Septum With Borderline Tricuspid Valve: How Small Is Too Small.

LaPar DJ, Bacha E

Seminars in thoracic and cardiovascular surgery. Pediatric cardiac surgery annual 2019; (22()):27-31 doi:10.1053/j.pcsu.2019.02.007.

Ductal stenting to improve pulmonary blood flow in pulmonary atresia with intact ventricular septum and critical pulmonary stenosis after balloon valvuloplasty.

Haddad RN, Hanna N, Charbel R, et al.

Cardiology in the young 2019; (29(4)):492-498 doi:10.1017/S1047951119000118.

Prediction of heart failure and death in an adult population of Fontan patients.

Sieweke JT, Haghikia A, Riehle C, et al.

Cardiology in the young 2019; (29(5)):602-609 doi:10.1017/S1047951119000258.

Perforation of the atretic pulmonary valve using chronic total occlusion (CTO) wire and coronary microcatheter.

Lefort B, Saint-Etienne C, Soulé N, et al.

Congenital heart disease 2019; (14(5)):814-818 doi:10.1111/chd.12812.

Right Ventricle-Dependent Coronary Circulation: Location of Obstruction Is Associated With Survival.

Spigel ZA, Qureshi AM, Morris SA, et al.

The Annals of thoracic surgery 2020; (109(5)):1480-1487 doi:10.1016/j.athoracsur.2019.08.066.

Prenatal echocardiographic classification and prognostic evaluation strategy in fetal pulmonary atresia with intact ventricular septum.

Liu L, Wang H, Cui C, et al.

Medicine 2019; (98(42)):e17492 doi:10.1097/MD.0000000000017492.

Neonatal Pulmonary Atresia With Intact Ventricular Septum-8-Year Surgical Experience at One Center.

Guanhua L, Jianzheng C, Gang X, et al.

The Journal of surgical research 2020; (251()):38-46 doi:10.1016/j.jss.2020.01.017.

Hybrid Approach to Right Ventricle Decompression in Muscular Pulmonary Atresia with Intact Ventricular Septum.

Mohammad Nijres B, Al-Khatib Y, Baliulis G, et al.

Pediatric cardiology 2020; (41(6)):1238-1241 doi:10.1007/s00246-020-02364-5.

Transcatheter radiofrequency pulmonary valve perforation in newborns with pulmonary atresia/intact ventricular septum: Echocardiographic predictors of biventricular circulation.

Yoldaş T, Örün UA, Doğan V, et al.

Echocardiography (Mount Kisco, N.Y.) 2020; (37(8)):1258-1264 doi:10.1111/echo.14811.

Low-dose prostaglandin E1 is safe and effective for critical congenital heart disease: is it time to revisit the dosing guidelines?

Vari D, Xiao W, Behere S, et al.

Cardiology in the young 2021; (31(1)):63-70 doi:10.1017/S1047951120003297.

Decline Is Not Inevitable: Exercise Capacity Trajectory in an Australian and New Zealand Fontan Cohort.

Tran DL, Rodrigues C, du Plessis K, et al.

Heart, lung & circulation 2021; (30(9)):1356-1363 doi:10.1016/j.hlc.2021.01.004.

Role alteration predicts anxiety and depressive symptoms in parents of infants with congenital heart disease: a pilot study.

Lisanti AJ, Kumar A, Quinn R, et al.

Cardiology in the young 2021; (31(11)):1842-1849 doi:10.1017/S1047951121001037.

Heterogeneous outcomes of liver disease after heart transplantation for a failed Fontan procedure.

Ybarra AM, Khanna G, Turmelle YP, et al.

Pediatric transplantation 2021; (25(8)):e14094 doi:10.1111/petr.14094.

Systemic Venous Hypertension and Low Output Are Prevalent at Catheterization in Adults with Pulmonary Atresia and Intact Ventricular Septum Regardless of Repair Strategy.

Jain CC, Egbe AC, Stephens EH, et al.

Seminars in thoracic and cardiovascular surgery 2022; (34(4)):1312-1319 doi:10.1053/j.semtcvs.2021.10.006.

Commentary: Despite best intentions: Developing better strategies for patients with pulmonary atresia with intact ventricular septum.

Barron DJ, Vanderlaan RD

The Journal of thoracic and cardiovascular surgery 2022; (164(5)):1289-1290 doi:10.1016/j.jtcvs.2021.12.038.

Management of Patients With Single-Ventricle Physiology Across the Lifespan: Contributions From Magnetic Resonance and Computed Tomography Imaging.

Lam CZ, Nguyen ET, Yoo SJ, Wald RM

The Canadian journal of cardiology 2022; (38(7)):946-962 doi:10.1016/j.cjca.2022.01.011.

Very preterm and very low birthweight infant with pulmonary atresia intact ventricular septum, right ventricle-dependent coronary circulation, and discontinuous pulmonary arteries.

Puente BN, d'Udekem Y, Krishnan A

Cardiology in the young 2022; (32(9)):1530-1532 doi:10.1017/S1047951122000038.

Pulmonary atresia with intact ventricular septum: Intended strategies.

Sukhavasi A, McHugh-Grant S, Glatz AC, et al.

The Journal of thoracic and cardiovascular surgery 2022; (164(5)):1277-1288 doi:10.1016/j.jtcvs.2021.11.104.

Pulmonary Atresia with Intact Ventricular Septum: Midterm Outcomes from a Multicenter Cohort.

Iliopoulos I, Mastropietro CW, Flores S, et al.

Pediatric cardiology 2024; (45(4)):847-857 doi:10.1007/s00246-022-02954-5.

Patent Ductus Arteriosus Stent Versus Surgical Aortopulmonary Shunt for Initial Palliation of Cyanotic Congenital Heart Disease with Ductal-Dependent Pulmonary Blood Flow: A Systematic Review and Meta-Analysis.

Tseng SY, Truong VT, Peck D, et al.

Journal of the American Heart Association 2022; (11(13)):e024721 doi:10.1161/JAHA.121.024721.

Generation of an induced pluripotent stem cell line NCHi003-A from a 11-year-old male with pulmonary atresia with intact ventricular septum (PA-IVS).

Contreras J, Alonzo M, Ye S, et al.

Stem cell research 2022; (64()):102893 doi:10.1016/j.scr.2022.102893.

Procedural Outcomes of Pulmonary Atresia With Intact Ventricular Septum in Neonates: A Multicenter Study.

Cheung EW, Mastropietro CW, Flores S, et al.

The Annals of thoracic surgery 2023; (115(6)):1470-1477 doi:10.1016/j.athoracsur.2022.07.055.

Computed Tomographic Angiography Provides Reliable Coronary Artery Evaluation in Infants With Pulmonary Atresia Intact Ventricular Septum.

Malone LJ, Browne LP, Morgan GJ, et al.

Seminars in thoracic and cardiovascular surgery 2024; (36(3)):336-344 doi:10.1053/j.semtcvs.2022.10.003.

The Utility of CT Angiography in Neonates with Pulmonary Atresia with Intact Ventricular Septum and Concern for Right Ventricular Dependent Coronary Circulation: Case Series.

Boucek K, Hlavacek A

Pediatric cardiology 2023; (44(6)):1342-1349 doi:10.1007/s00246-022-03055-z.

Perfusion Strategy to Prevent Right Ventricular Decompression on Cardiopulmonary Bypass During Extracardiac Fontan for Right Ventricle-Dependent Coronary Circulation.

Joshi RK, Aggarwal N, Agarwal M, et al.

World journal for pediatric & congenital heart surgery 2023; (14(4)):500-502 doi:10.1177/21501351231162894.

The so-called "one-and-a-half" ventricular repair: where are we after 40 years?

Chowdhury UK, Anderson RH, Pandey NN, et al.

Cardiology in the young 2023; (33(9)):1497-1505 doi:10.1017/S1047951123001646.

Transcatheter Ductal Stents Versus Surgical Systemic-Pulmonary Artery Shunts in Neonates With Congenital Heart Disease With Ductal-Dependent Pulmonary Blood Flow: Trends and Associated Outcomes From the Pediatric Health Information System Database.

Valencia E, Staffa SJ, Kuntz MT, et al.

Journal of the American Heart Association 2023; (12(17)):e030528 doi:10.1161/JAHA.123.030528.

Radiofrequency Perforation of an Atretic Pulmonary Valve with a Modified Coronary Wire and Electrocautery Pencil.

Mejia E, Soszyn N, Morgan GJ, Leahy RA

Pediatric cardiology 2024; (45(7)):1607-1609 doi:10.1007/s00246-023-03270-2.

Cumulative Dose of Prostaglandin E1 Determines Gastrointestinal Adverse Effects in Term and Near-Term Neonates Awaiting Cardiac Surgery: A Retrospective Cohort Study.

Ofek Shlomai N, Lazarovitz G, Koplewitz B, Eventov Friedman S

Children (Basel, Switzerland) 2023; (10(9)) doi:10.3390/children10091572.

Blalock-Taussig Shunt versus Ductal Stenting as Palliation for Duct-Dependent Pulmonary Circulation.

Al Kindi H, Al Harthi H, Al Balushi A, et al.

Sultan Qaboos University medical journal 2023; (23(Spec Iss)):10-15 doi:10.18295/squmj.12.2023.073.

Effectiveness of Alprostadil for Ductal Patency.

Gordon CM, Tan JT, Carr RR

The journal of pediatric pharmacology and therapeutics : JPPT : the official journal of PPAG 2024; (29(1)):37-44 doi:10.5863/1551-6776-29.1.37.

A case report of pulmonary atresia with intact ventricular septum: an extraordinary finding of subsystemic right ventricle.

Luo G, Liu A, Sun H, et al.

Frontiers in pediatrics 2024; (12()):1251274 doi:10.3389/fped.2024.1251274.

Comparison of Ductal Stent Versus Surgical Shunt as Initial Intervention for Neonates with Pulmonary Atresia with Intact Ventricular Septum.

Puente BN, Mastropietro CW, Flores S, et al.

Pediatric cardiology 2024; doi:10.1007/s00246-024-03529-2.

Pulmonary Atresia with Intact Ventricular Septum: Correlation of Preoperative Computed Tomography-Derived Parameters with Echocardiographic Tricuspid Valve Z-Score and Surgical Outcomes.

Goo HW, Park SH, Goo SY

Pediatric cardiology 2025; (46(6)):1560-1569 doi:10.1007/s00246-024-03570-1.

Comparison of Immediate Intensive Care Outcomes of Patent Ductus Arteriosus Stenting Versus Modified Blalock-Taussig-Thomas Shunt in Infants With Ductal-Dependent Pulmonary Circulation.

Sirisani JD, Haranal M, Soo KW, et al.

Pediatric cardiology 2024; doi:10.1007/s00246-024-03591-w.

[Right ventricle-dependent coronary circulation in pulmonary atresia with intact ventricular septum. About three patients without coronary ostium atresia. Is a transient percutaneous decompression maneuver necessary?]

Colín-Ortiz JL, López-Andrade CE

Archivos de cardiologia de Mexico 2024; doi:10.24875/ACM.24000057.

Coronary Artery Disease and Microvascular Ischemia in Patients with Cardiac Amyloidosis.

Itzhaki Ben Zadok O, Vaxman I, Hoss S, et al.

Acta haematologica 2025; (148(4)):452-461 doi:10.1159/000542510.

Myocardial ischemia risk in Fontan candidates with pulmonary atresia with intact ventricular septum.

Masaki N, Tatewaki H, Matsuo S, et al.

General thoracic and cardiovascular surgery 2025; (73(9)):675-681 doi:10.1007/s11748-025-02131-4.

Fontan-Associated Liver Disease (FALD) in the EUROFontan Experience. An Insight into European Awareness.

Gozzi A, Vedovelli L, Bergonzoni E, et al.

Pediatric cardiology 2025; doi:10.1007/s00246-025-03781-0.

Echocardiographic Assessment of Cardiac Phenotype Predicts Complications and Guides Intensive Care Management Following Pulmonary Valve Balloon Dilation in Neonates With Pulmonary Atresia/Critical Pulmonary Stenosis With Intact Ventricular Septum.

Moras P, Luciano P, Campanale CM, et al.

Echocardiography (Mount Kisco, N.Y.) 2025; (42(5)):e70182 doi:10.1111/echo.70182.

Role of Computed Tomography Findings in Diagnosing Pulmonary Atresia With Intact Ventricular Septum and Right Ventricle-Dependent Coronary Circulation: A Case Report.

Thurmann KE, Richardson RR

Cureus 2025; (17(5)):e83914 doi:10.7759/cureus.83914.

Parents' experiences and psychosocial problems related to their preterm infants with congenital heart disease hospitalized in the neonatal intensive care unit: A descriptive phenomenological study.

Sabaz N, Ciydem E, Tosun S, et al.

Journal of pediatric nursing 2026; (86()):383-395 doi:10.1016/j.pedn.2025.11.033.