Research & Literature

Esophageal involvement by pemphigus vulgaris resulting in dysphagia.

Cecinato P, Laterza L, De Marco L, et al.

Endoscopy 2015; (47 Suppl 1 UCTN()):E271-2 doi:10.1055/s-0034-1391905.

Management of pemphigus vulgaris: challenges and solutions.

Gregoriou S, Efthymiou O, Stefanaki C, Rigopoulos D

Clinical, cosmetic and investigational dermatology 2015; (8()):521-7 doi:10.2147/CCID.S75908.

Pemphigus: An Ophthalmological Review.

Chirinos-Saldaña P, Navas A, Ramírez-Miranda A, et al.

Eye & contact lens 2016; (42(2)):91-8 doi:10.1097/ICL.0000000000000155.

Long-Term Remissions in Recalcitrant Pemphigus Vulgaris.

Ahmed AR, Kaveri S, Spigelman Z

The New England journal of medicine 2015; (373(27)):2693-4 doi:10.1056/NEJMc1508234.

Oral Pemphigus Vulgaris: Case Report.

Arpita R, Monica A, Venkatesh N, et al.

Ethiopian journal of health sciences 2015; (25(4)):367-72.

Concomitant pemphigus vulgaris and pemphigoid gestationis: a case report and review of the literature.

Vin H, Seyfer SJ, McClain CM, Hsu S

Dermatology online journal 2016; (22(1)).

Monopathogenic vs multipathogenic explanations of pemphigus pathophysiology.

Ahmed AR, Carrozzo M, Caux F, et al.

Experimental dermatology 2016; (25(11)):839-846 doi:10.1111/exd.13106.

Oral mucous membrane pemphigoid and pemphigus vulgaris-a retrospective two-center cohort study.

Sultan AS, Villa A, Saavedra AP, et al.

Oral diseases 2017; (23(4)):498-504 doi:10.1111/odi.12639.

Evidence for a role of eosinophils in blister formation in bullous pemphigoid.

de Graauw E, Sitaru C, Horn M, et al.

Allergy 2017; (72(7)):1105-1113 doi:10.1111/all.13131.

Low-dose rituximab and concurrent adjuvant therapy for pemphigus: Protocol and single-centre long-term review of nine patients.

Robinson AJ, Vu M, Unglik GA, et al.

The Australasian journal of dermatology 2018; (59(1)):e47-e52 doi:10.1111/ajd.12571.

Nasal, oral, and pharyngolaryngeal manifestations of pemphigus vulgaris: Endoscopic ororhinolaryngologic examination.

Ohki M, Kikuchi S

Ear, nose, & throat journal 2017; (96(3)):120-127 doi:10.1177/014556131709600311.

Identification of factors associated with treatment refractoriness of oral lesions in pemphigus vulgaris.

Kumar S, De D, Handa S, et al.

The British journal of dermatology 2017; (177(6)):1583-1589 doi:10.1111/bjd.15658.

Rituximab: A Magic Bullet for Pemphigus.

Anandan V, Jameela WA, Sowmiya R, et al.

Journal of clinical and diagnostic research : JCDR 2017; (11(4)):WC01-WC06 doi:10.7860/JCDR/2017/21868.9717.

Bullous pemphigoid and pemphigus vulgaris.

Kayani M, Aslam AM

BMJ (Clinical research ed.) 2017; (357()):j2169 doi:10.1136/bmj.j2169.

Inhibition of p38MAPK signalling prevents epidermal blistering and alterations of desmosome structure induced by pemphigus autoantibodies in human epidermis.

Egu DT, Walter E, Spindler V, Waschke J

The British journal of dermatology 2017; (177(6)):1612-1618 doi:10.1111/bjd.15721.

Clinical Implications of Direct Immunofluorescence Findings in Patients With Ocular Mucous Membrane Pemphigoid.

Labowsky MT, Stinnett SS, Liss J, et al.

American journal of ophthalmology 2017; (183()):48-55 doi:10.1016/j.ajo.2017.08.009.

British Association of Dermatologists' guidelines for the management of pemphigus vulgaris 2017.

Harman KE, Brown D, Exton LS, et al.

The British journal of dermatology 2017; (177(5)):1170-1201 doi:10.1111/bjd.15930.

An Oral Disease Severity Score validated for use in oral pemphigus vulgaris.

Ormond M, McParland H, Donaldson ANA, et al.

The British journal of dermatology 2018; (179(4)):872-881 doi:10.1111/bjd.16265.

Comparison of individually tailored versus fixed-schedule rituximab regimen to maintain ANCA-associated vasculitis remission: results of a multicentre, randomised controlled, phase III trial (MAINRITSAN2).

Charles P, Terrier B, Perrodeau É, et al.

Annals of the rheumatic diseases 2018; (77(8)):1143-1149 doi:10.1136/annrheumdis-2017-212878.

Evaluation of the Importance of Immunological Profile for Pemphigus Vulgaris in the Light of Necessity to Modify Compensation Theory.

Öktem A, Hayran Y, Uysal Pİ, et al.

Acta dermatovenerologica Croatica : ADC 2018; (26(2)):100-104.

Retrospective analysis of a single-center clinical experience toward development of curative treatment of 123 pemphigus patients with a long-term follow-up: efficacy and safety of the multidrug protocol combining intravenous immunoglobulin with the cytotoxic immunosuppressor and mitochondrion-protecting drugs.

Grando SA

International journal of dermatology 2019; (58(1)):114-125 doi:10.1111/ijd.14143.

Distinguishing histopathologic features of acantholytic dermatoses and the pattern of acantholytic hypergranulosis.

See SHC, Peternel S, Adams D, North JP

Journal of cutaneous pathology 2019; (46(1)):6-15 doi:10.1111/cup.13356.

Incidence and death rate of pemphigus vulgaris and pemphigus foliaceus in Korea: A nationwide, population-based study (2006-2015).

Lee YB, Lee JH, Lee SY, et al.

The Journal of dermatology 2018; (45(12)):1396-1402 doi:10.1111/1346-8138.14667.

[Ultrastructure of epidermocytes in true pemphigus acantholysis].

Lykova SG, Marinkin IO, Nemchaninova OB, et al.

Arkhiv patologii 2019; (81(1)):3-8 doi:10.17116/patol2019810113.

Review of autoimmune blistering diseases: the Pemphigoid diseases.

Daniel BS, Murrell DF

Journal of the European Academy of Dermatology and Venereology : JEADV 2019; (33(9)):1685-1694 doi:10.1111/jdv.15679.

Oral autoimmune vesicobullous diseases: Classification, clinical presentations, molecular mechanisms, diagnostic algorithms, and management.

Leuci S, Ruoppo E, Adamo D, et al.

Periodontology 2000 2019; (80(1)):77-88 doi:10.1111/prd.12263.

Quality of life remains poor for patients with pemphigus vulgaris despite targeted therapies.

Schultz B, Latour E, Fett N

The British journal of dermatology 2019; (181(5)):1101-1103 doi:10.1111/bjd.18167.

Consensus on the treatment of autoimmune bullous dermatoses: pemphigus vulgaris and pemphigus foliaceus - Brazilian Society of Dermatology.

Porro AM, Hans Filho G, Santi CG

Anais brasileiros de dermatologia 2019; (94(2 Suppl 1)):20-32 doi:10.1590/abd1806-4841.2019940206.

Pemphigus vulgaris disease activity: The role of antibodies to desmogleins and their isotype.

Yeoh SC, Byth-Wilson K, Murrell DF, et al.

Journal of oral pathology & medicine : official publication of the International Association of Oral Pathologists and the American Academy of Oral Pathology 2019; (48(7)):619-625 doi:10.1111/jop.12913.

Acantholysis may precede elevation of circulating anti-desmoglein 3 antibody levels in pemphigus vulgaris presenting with desquamative gingivitis.

Endo H, Rees TD, Niwa H, et al.

Clinical and experimental dental research 2019; (5(3)):219-224 doi:10.1002/cre2.174.

Oral Lesions in Autoimmune Bullous Diseases: An Overview of Clinical Characteristics and Diagnostic Algorithm.

Rashid H, Lamberts A, Diercks GFH, et al.

American journal of clinical dermatology 2019; (20(6)):847-861 doi:10.1007/s40257-019-00461-7.

The involvement of ADAM10 in acantholysis in mucocutaneous pemphigus vulgaris depends on the autoantibody profile of each patient.

Ivars M, España A, Alzuguren P, et al.

The British journal of dermatology 2020; (182(5)):1194-1204 doi:10.1111/bjd.18382.

Rituximab is an effective treatment in patients with pemphigus vulgaris and demonstrates a steroid-sparing effect.

Chen DM, Odueyungbo A, Csinady E, et al.

The British journal of dermatology 2020; (182(5)):1111-1119 doi:10.1111/bjd.18482.

Pemphigus.

Schmidt E, Kasperkiewicz M, Joly P

Lancet (London, England) 2019; (394(10201)):882-894 doi:10.1016/S0140-6736(19)31778-7.

Evaluation of the pathogenicity of anti-desmoglein antibodies of pemphigus vulgaris patients using human organ culture assay.

Saleh AM, El-Samanoudy SI, Rashed LA, Saleh MA

Archives of dermatological research 2020; (312(4)):289-294 doi:10.1007/s00403-019-01988-9.

Mucocutaneous Diseases.

Kuten-Shorrer M, Menon RS, Lerman MA

Dental clinics of North America 2020; (64(1)):139-162 doi:10.1016/j.cden.2019.08.009.

Pemphigus vulgaris - approach and management.

Popescu IA, Statescu L, Vata D, et al.

Experimental and therapeutic medicine 2019; (18(6)):5056-5060 doi:10.3892/etm.2019.7964.

Nikolsky's sign: A pathognomic boon.

Maity S, Banerjee I, Sinha R, et al.

Journal of family medicine and primary care 2020; (9(2)):526-530 doi:10.4103/jfmpc.jfmpc_889_19.

Update on IgG4-mediated autoimmune diseases: New insights and new family members.

Koneczny I

Autoimmunity reviews 2020; (19(10)):102646 doi:10.1016/j.autrev.2020.102646.

Serum levels of soluble PD1 in pemphigus vulgaris: A useful marker for disease severity.

Zeid OA, Rashed L, Khalifa S, et al.

Journal of cosmetic dermatology 2021; (20(4)):1298-1302 doi:10.1111/jocd.13719.

A retrospective cohort study reporting rituximab treatment for 33 patients with immunobullous disease.

Watson N, Carrozzo M, Hampton P

Journal of oral pathology & medicine : official publication of the International Association of Oral Pathologists and the American Academy of Oral Pathology 2021; (50(1)):92-97 doi:10.1111/jop.13123.

The health-related quality of life and psychological profile in patients with oropharyngeal Pemphigus Vulgaris in complete clinical remission: A case-control study.

Calabria E, Adamo D, Leuci S, et al.

Journal of oral pathology & medicine : official publication of the International Association of Oral Pathologists and the American Academy of Oral Pathology 2021; (50(5)):510-519 doi:10.1111/jop.13150.

Prevalence of oral mucosal lesions in patients with pemphigus vulgaris: A systematic review and meta-analysis.

Batistella EÂ, Sabino da Silva R, Rivero ERC, Silva CAB

Journal of oral pathology & medicine : official publication of the International Association of Oral Pathologists and the American Academy of Oral Pathology 2021; (50(8)):750-757 doi:10.1111/jop.13167.

Pemphigus Vulgaris and Bullous Pemphigoid of the Upper Aerodigestive Tract: A Review Article and Novel Approaches to Management.

Hussain MH, Tanweer F, Sakagiannis G, et al.

ORL; journal for oto-rhino-laryngology and its related specialties 2021; (83(6)):395-403 doi:10.1159/000515229.

[Clinical Analysis of Eight Cases of Pemphigus with High Titers of Anti-desmoglein Antibodies in Remission].

Jin XX, Li SZ, Zuo YG, Jin HZ

Zhongguo yi xue ke xue yuan xue bao. Acta Academiae Medicinae Sinicae 2021; (43(2)):166-172 doi:10.3881/j.issn.1000-503X.13452.

Rituximab versus Mycophenolate Mofetil in Patients with Pemphigus Vulgaris.

Werth VP, Joly P, Mimouni D, et al.

The New England journal of medicine 2021; (384(24)):2295-2305 doi:10.1056/NEJMoa2028564.

Current status and prospects for the diagnosis of pemphigus vulgaris.

Nili A, Salehi Farid A, Asgari M, et al.

Expert review of clinical immunology 2021; (17(8)):819-834 doi:10.1080/1744666X.2021.1945925.

A Comparative Study to Evaluate the Efficacy and Cost of Rituximab versus Dexamethasone Cyclophosphamide Pulse in Patients of Pemphigus Vulgaris.

Das S, Agarwal K, Singh S, et al.

Indian journal of dermatology 2021; (66(2)):223 doi:10.4103/ijd.IJD_306_20.

Biologics in autoimmune bullous diseases: Current scenario.

Bishnoi A, De D, Handa S, Mahajan R

Indian journal of dermatology, venereology and leprology 2021; (87(5)):611-620.

Temporal Outcomes after Rituximab Therapy for Pemphigus Vulgaris.

Tovanabutra N, Bax CE, Feng R, et al.

The Journal of investigative dermatology 2022; (142(4)):1058-1064.e7 doi:10.1016/j.jid.2021.09.013.

Treatment of pemphigus in Australia: Aligning current practises with global recommendations.

Somerville E, Gebauer K, Mclean-Tooke A

The Australasian journal of dermatology 2022; (63(2)):190-196 doi:10.1111/ajd.13804.

Pemphigus Vulgaris: Present and Future Therapeutic Strategies.

Didona D, Paolino G, Di Zenzo G, et al.

Dermatology practical & conceptual 2022; (12(1)):e2022037 doi:10.5826/dpc.1201a37.

HLA-DRB1 and DQB1 genetic susceptibility to pemphigus vulgaris and pemphigus foliaceus in Vietnamese patients.

Vuong TBT, Do DM, Ong PT, Thanh Le TV

Dermatology reports 2022; (14(2)):9286 doi:10.4081/dr.2021.9286.

Burden of pemphigus vulgaris with a particular focus on women: A review.

Kianfar N, Dasdar S, Mahmoudi H, Daneshpazhooh M

International journal of women's dermatology 2022; (8(3)):e056 doi:10.1097/JW9.0000000000000056.

Desmoglein compensation hypothesis fidelity assessment in Pemphigus.

Sielski L, Baker J, DePasquale MC, et al.

Frontiers in immunology 2022; (13()):969278 doi:10.3389/fimmu.2022.969278.

Detection of anti-desmoglein antibodies in oral lichen planus: What do we know so far.

Didona D, Hertl M

Frontiers in immunology 2022; (13()):1001970 doi:10.3389/fimmu.2022.1001970.

The Global Incidence Rate of Pemphigus Vulgaris: A Systematic Review and Meta-Analysis.

Zhao L, Chen Y, Wang M

Dermatology (Basel, Switzerland) 2023; (239(4)):514-522 doi:10.1159/000530121.

Paraneoplastic Pemphigus Mimicking Pemphigus Vulgaris Associated With Castleman Disease.

Grigore M, Costache M, Simionescu O

Cureus 2023; (15(3)):e36114 doi:10.7759/cureus.36114.

A rare case of pemphigus vulgaris disguised as a malignant gingival ulcer.

Chen J, Tang H, Zhang D, et al.

BMC oral health 2023; (23(1)):319 doi:10.1186/s12903-023-02980-6.

Optimal biopsy site for the diagnosis of oral pemphigus vulgaris and mucous membrane pemphigoid: a systematic review and meta-analysis.

Zeng Q, Liu J, Mu J, et al.

International journal of oral and maxillofacial surgery 2023; (52(11)):1162-1172 doi:10.1016/j.ijom.2023.05.005.

Serologic Biomarkers in Pemphigus Monitoring: C-reactive Protein, Macrophage Migration Inhibitory Factor, and Prolactin Levels Versus Autoantibody Assays.

Mortazavi H, Saeidi V, Balighi K, et al.

Iranian journal of allergy, asthma, and immunology 2023; (22(3)):312-318 doi:10.18502/ijaai.v22i3.13059.

A case report of esophageal cancer in a patient with pemphigus vulgaris: A coincidence or something beyond that?

Balighi K, Aryanian Z, Balighi S, et al.

Cancer reports (Hoboken, N.J.) 2023; (6(12)):e1896 doi:10.1002/cnr2.1896.

Rituximab as a maintenance treatment in patients with pemphigus vulgaris: When is the right time for discontinuation?

Aryanian Z, Balighi K, Emadi SN, Hatami P

Journal of cosmetic dermatology 2024; (23(2)):406-408 doi:10.1111/jocd.16030.

Anal involvement in patient with pemphigus vulgaris: Case report.

Núñez-Rocha RE, Andrade-Restrepo J, Gómez-Carrillo D, et al.

International journal of surgery case reports 2024; (114()):109185 doi:10.1016/j.ijscr.2023.109185.

Direct Immunofluorescence of Skin and Oral Mucosa: Guidelines for Selecting the Optimum Biopsy Site.

Mahmood MN

Dermatopathology (Basel, Switzerland) 2024; (11(1)):52-61 doi:10.3390/dermatopathology11010006.

Beyond the Surface: A Clinical Insight Into a 60-Year-Old Male With Pemphigus vulgaris.

Akel M, Wright M, Aladum B, Hernandez Borges S

Cureus 2024; (16(2)):e54408 doi:10.7759/cureus.54408.

The evolution of Pemphigus publications: A bibliometric analysis with research trends and global productivity.

Öztekin A, Öztekin C

Medicine 2024; (103(18)):e38047 doi:10.1097/MD.0000000000038047.

Evaluation of the Quality of Life and the Demographic and Clinical Characteristics of Patients With Pemphigus With Oral Mucosal İnvolvement: A Multicenter Observational Study.

Polat AK, Mülayim MK, Gür TF, et al.

Dermatology practical & conceptual 2024; (14(2)) doi:10.5826/dpc.1402a99.

Prognostic Factors Predicting Remission Following Rituximab Therapy for Pemphigus Vulgaris.

Raviv T, Pevzner K, Barzilai A, et al.

Acta dermato-venereologica 2025; (105()):adv27140 doi:10.2340/actadv.v105.27140.

Pemphigus Vulgaris: Clinical Aspects and Treatments.

Geng RSQ, Sibbald RG

Advances in skin & wound care 2025; (38(5)):232-238 doi:10.1097/ASW.0000000000000307.

Unusual Presentation of Pemphigus Vulgaris as a Solitary Ulcerative Scalp Lesion: A Case Report.

Nejjari S, Basri G, Chikhaoui I, et al.

Cureus 2025; (17(6)):e87025 doi:10.7759/cureus.87025.

A 10-Year Observational Study on Treatment Approaches in Pemphigus and Pemphigoid.

Pereira CP, Santos R, Ferreira L, et al.

Acta stomatologica Croatica 2025; (59(2)):190-198 doi:10.15644/asc59/2/8.

A Case Report of Pemphigus Vulgaris Initially Misdiagnosed as Tinea Capitis: Infectious Consequences of Diagnostic Delay in a Patient Treated With Rituximab.

González-Rodríguez JC, Cristofori M, Antunez Oliva JA, Cortés-Marín EE

Cureus 2025; (17(7)):e87662 doi:10.7759/cureus.87662.

Clinical practice guidelines for rituximab treatment in children with steroid-sensitive nephrotic syndrome.

Shen Q, Xia ZK, Liu JL, et al.

World journal of pediatrics : WJP 2025; (21(8)):775-791 doi:10.1007/s12519-025-00957-9.

Patient-Reported Outcomes on Quality of Life in Older Adults with Oral Pemphigus.

Russu EA, Popa LG, Păunică S, et al.

Healthcare (Basel, Switzerland) 2025; (13(22)) doi:10.3390/healthcare13222843.

Radiotherapy-induced pemphigus vulgaris: a challenging case of extensive mucocutaneous ulcerations and literature review.

Santos BC, Ferraz DLF, Eleuterio MH, et al.

Oral surgery, oral medicine, oral pathology and oral radiology 2026; (141(4)):495-502 doi:10.1016/j.oooo.2025.11.004.

[Value of direct immunofluorescence in the diagnosis of oral mucosal pemphigus vulgaris: A retrospective study based on multi-index combined analysis].

Chi Y, Jiang H, Chen Y, et al.

Beijing da xue xue bao. Yi xue ban = Journal of Peking University. Health sciences 2026; (58(1)):68-73.

Anti-Desmoglein 3 Avidity Correlates Better With Pemphigus Vulgaris Severity Than Anti-Desmoglein 3 Concentration.

Lekic B, Bonaci-Nikolic B, Lalosevic J, et al.

International journal of dermatology 2026; doi:10.1111/ijd.70322.